1/12. Isolated true atherosclerotic aneurysm of the profunda femoris artery. Case report.The authors report a case of true isolated atherosclerotic aneurysm of the profunda femoris artery. On the basis of a careful search of the literature some aspects of this rare disease are illuminated in terms of its low incidence, pathologic background and treatment; the last should always be aggressive due to the high possibility (about 50%) of major complications mainly represented by rupture. Simple aneurysmectomy without flow re-establishment may be allowed only if the femoropopliteal tract is normal- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
2/12. Multiple renal artery aneurysms diagnosed by three-dimensional CT angiography.renal artery aneurysm is a relatively rare disease that is found in 0.3--1.0% of patients examined by renal angiography. We report a case of multiple renal artery aneurysms that were accurately diagnosed by three-dimensional CT angiography (3D-CTA) using volumetric data sets of spiral CT.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
3/12. Extracranial carotid aneurysm in Takayasu's arteritis.Extracranial carotid aneurysm caused by Takayasu's arteritis is extremely rare. We have experienced six cases of extracranial carotid aneurysm among 106 cases of Takayasu's arteritis that were treated surgically in the past 50 years. We herein review these cases and discuss the surgical indications and postoperative course of this rare disease. We report original observations about extracranial carotid aneurysm in Takayasu's arteritis.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
4/12. Idiopathic pulmonary artery aneurysm: digital subtraction pulmonary angiography grossly underestimates the size of the aneurysm.pulmonary artery aneurysm is a rare disease entity. The majority of cases are associated with congenital cardiovascular diseases, infection, and trauma; idiopathic pulmonary artery aneurysm is extremely rare. Although conventional and digital subtraction pulmonary angiography remains as the imaging modality of choice for the pulmonary vessels, it is invasive and sometimes may be inaccurate. With the advent of spiral computed tomographic angiography (CTA), pulmonary artery aneurysm can be diagnosed noninvasively and accurately. We report a case of a 68-year-old man with idiopathic pulmonary artery aneurysm of the descending branch of right pulmonary artery where the true caliber of the aneurysm was significantly underestimated in the digital subtraction pulmonary angiography. The literatures of this rare condition are reviewed with the emphasis on the application of CTA in this disease.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
5/12. Combined percutaneous endovascular and open surgical approach in the treatment of a persistent sciatic artery aneurysm presenting with acute limb-threatening ischemia--a case report and review of the literature.Persistent sciatic artery (PSA) is a continuation of the internal iliac artery into the popliteal-tibial vessels and provides the major supply to the lower limb bud in early embryologic development, and its remnants participate in the formation of the inferior gluteal, deep femoral, popliteal, peroneal, and pedal vessels. When the femoral artery develops, the PSA involutes. In rare circumstances it persists and has a bilateral location in 22% of cases of PSA. This rare vascular anomaly is associated with aneurysmal formation in 15% to 46% of cases. Persistent sciatic artery aneurysm (PSAA) was first described in 1864. At present 87 cases, including this case, have been reported in the international literature. The authors describe a patient affected with PSAA and treated with a combination of thrombolysis, arterial reconstruction, and aneurysm embolization in a staged fashion. embryology, anatomy, pathology, clinical presentation, diagnosis, and treatment of this rare disease are briefly discussed.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
6/12. The hypothenar hammer syndrome.The hypothenar hammer syndrome is manifested as digital ischaemia. It is caused by trauma to the ulnar arteries in workmen who use their hands as a mallet, and is not a rare disease. The pathophysiology of the disease is reviewed, with illustrative cases. The hypothenar hammer syndrome should be considered as a compensable injury.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
7/12. Osler-Weber-Rendu disease--unexpected complication following excision of splenic aneurysm--a case report.Osler-Weber-Rendu disease is an autosomal dominant disease, sometimes known as hereditary hemorrhagic telangiectasia (HHT) with a family history. It is a rare disease and there are no records of families with inheritance lineage in Riyadh. We experienced an anesthetic management of a 28-yr-old woman with Osler-Weber-Rendu disease. She was diagnosed to have splenic aneurysm and was scheduled for excision of splenic aneurysm. A chest X-ray revealed pulmonary arterio-venous malformation all over the lungs. The anesthesia and surgery went deliberately smooth with selective period of intensive care admission. In the intermediate post operative period, however, she was diagnosed as having pleural effusion. A chest drain was inserted as an emergency, but the patient developed tension pneumothorax, which necessitated resuscitation and readmission to intensive care Unit. lung atelactasis was diagnosed. Attendance by qualified surgical night staff, communication, vigilance and consultations are as important as the proper management of such rare cases.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
8/12. An unusual presentation of classic polyarteritis nodosa in a child.Classic polyarteritis nodosa (c-PAN) is a rare disease in adults and extremely rare in children. We report a 3-year-old girl with c-PAN who presented with disturbances of consciousness and hypertension. Cranial tomography showed a subarachnoid hemorrhage. Subsequent magnetic resonance imaging and magnetic resonance angiography demonstrated subarachnoid hemorrhage and acute ischemic lesions. Renal angiography revealed bilateral multiple aneurysms. Due to her constitutional symptoms and hypertension and radiological findings she was diagnosed as having c-PAN. She was successfully treated with hydralazine followed by angiotensin-converting enzyme inhibitor, calcium channel blocker, intravenous pulse methylprednisolone, and subsequently oral prednisolone and oral cyclophosphamide. To our knowledge this is the youngest patient with c-PAN presenting with subarachnoid hemorrhage. Malign hypertension at this young age deserves a meticulous investigation of the vascular origin. Furthermore, treatment with pulse methyl prednisolone followed by oral prednisolone and oral cyclophosphamide is a successful modality of treatment in such a life-threatening presentation of c-PAN in childhood.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
9/12. splenic vein aneurysm with calcification of splenic and portal veins.splenic vein aneurysm is a rare disease, and calcifications in the portal venous system are also rare. Here we present a case of splenic vein aneurysm associated with calcification of the splenic and portal veins, a condition that to our knowledge has not been reported before.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
10/12. color duplex ultrasonography in detecting renal artery abnormalities in a patient with neurofibromatosis 1: a case report.Neurofibromatosis type 1 (NF1) is a rare disease; it involves not only the nervous system, but also both large and small arteries. Common vascular complications of NF1 include arterial stenosis, aneurysms, and arteriovenous fistulas involving the abdominal aorta and its branches. A coexisting left renal artery stenosis and aneurysm in a pediatric patient with NF1 was initially detected by color duplex ultrasonography in our institute.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
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