1/13. Marfan's syndrome, dextrocardia and situs inversus associated with discrete subaortic stenosis and aortic insufficiency in an adult female: case report.Marfan's syndrome is an inherited connective tissue defect that affects many organs, especially of the musculoskeletal, ophthalmic and cardiovascular systems, and may be associated with some rare conditions. Here, we report the first known case of Marfan's syndrome, combined with situs inversus totalis with dextrocardia and discrete subaortic stenosis and aortic insufficiency in a 22-year-old woman.- - - - - - - - - - ranking = 1keywords = stenosis (Clic here for more details about this article) |
2/13. Proximal isovelocity surface area (PISA) in the evaluation of fixed membranous subaortic stenosis.The evaluation of the severity of subaortic stenosis is usually expressed by the magnitude of the subvalvular gradient. Calculation of the membrane orifice area noninvasively is difficult by the standard means. We present a patient in whom the area was calculated using the proximal isovelocity surface area (PISA) method. This method should have clinical applicability because it is not flow dependent and can be used in patients with normal, reduced, or increased stroke volume.- - - - - - - - - - ranking = 1keywords = stenosis (Clic here for more details about this article) |
3/13. Mitral annular aneurysm resulting from subaortic muscle resection.We present a case of mitral annular aneurysm as a very rare complication developing soon after the surgical relief of subaortic stenosis. The cause of the aneurysm was considered to be the disruption of aorto-mitral intervalvular fibrosa at the initial operation. The surgical repair was successfully performed without compromising either aortic or mitral valvular functions. The preoperative transesophageal echocardiography was useful in delineating the precise anatomic features of this rare complication.- - - - - - - - - - ranking = 0.2keywords = stenosis (Clic here for more details about this article) |
4/13. Staged biventricular repair of Taussig-Bing anomaly with subaortic stenosis and coarctation of aorta.We present successful procedures for 2 infants who had the Taussig-Bing anomaly with subaortic stenosis and coarctation of the aorta. The initial procedure was coarctoplasty and the Damus-Kaye-Stansel procedure with modified Blalock-Taussig shunt. The second procedure was intraventricular repair (Kawashima procedure), Damus-Kaye-Stansel take-down and the reuse of native aortic and pulmonary valves 19 and 25 months later. Both patients survived the operations and postoperative hemodynamics were excellent at both 28 and 59 months follow-ups.- - - - - - - - - - ranking = 1keywords = stenosis (Clic here for more details about this article) |
5/13. Live three-dimensional transthoracic echocardiographic identification of discrete subaortic membranous stenosis.We describe an adult patient in whom live three-dimensional transthoracic echocardiography illustrated the exact site and full extent of the subaortic membrane as well as the narrow opening within the membrane, indicative of severe stenosis. To our knowledge this has not been reported previously.- - - - - - - - - - ranking = 1keywords = stenosis (Clic here for more details about this article) |
6/13. Transnasal placement of biplane transesophageal echocardiography probe intraoperatively in an adolescent with congenital heart disease.Intraoperative transesophageal echocardiography (TEE) is frequently used in children with congenital heart disease (CHD). Although transnasal TEE is being used in various settings in the adult population, there are no descriptions of its use intraoperatively in patients with CHD. This report describes the successful use of transnasal TEE after multiple unsuccessful transoral attempts in an adolescent male undergoing subaortic stenosis repair. IMPLICATIONS: Transnasal transesophageal echocardiography (TEE) is being used in various settings in the adult population. The author describes its use intraoperatively in an adolescent undergoing surgery for congenital heart disease after unsuccessful transoral attempts.- - - - - - - - - - ranking = 0.2keywords = stenosis (Clic here for more details about this article) |
7/13. Subaortic stenosis produced by an accessory mitral valve: the role of echocardiography.Subaortic stenosis caused by an accessory mitral valve is an exceedingly rare finding. We report the case of an asymptomatic 14-year-old patient, in whom transthoracic echocardiography revealed an accessory mitral valve in the left ventricular outflow tract, producing mild subaortic stenosis. Except for an aneurysm of the interventricular septum, with no shunt, there were no other anomalies. Transesophageal echocardiography provided details about the morphology and location of the accessory valve. Being asymptomatic and having only a mild gradient, antibiotic prophylaxis for infective endocarditis and follow-up were recommended. After 2 years the patient is asymptomatic, with a similar echocardiographic gradient.- - - - - - - - - - ranking = 1.2keywords = stenosis (Clic here for more details about this article) |
8/13. perioperative care of the patient with williams syndrome.williams syndrome, initially described by Williams, Barratt-Boyes, and Lowe in 1961, consists of characteristic dysmorphic features, congenital heart disease, and distinctive behavioral and emotional traits. In addition to acquired and congenital heart disease, manifestations in the renal, endocrine, musculoskeletal, and central nervous system may have implications during the perioperative period. Congenital and acquired heart disease can be a significant issue as sudden death, related to abnormalities of the coronary arteries, has been reported perioperatively in these patients. The authors present a 7-month-old infant, previously diagnosed with williams syndrome, who required anesthetic care for repair of subaortic and supravalvular aortic stenosis. The potential perioperative implications of williams syndrome are discussed.- - - - - - - - - - ranking = 0.2keywords = stenosis (Clic here for more details about this article) |
9/13. Subaortic obstruction and complete atrioventricular block in Behcet's disease.Left ventricular outflow tract obstruction may be dynamic, most commonly associated with hypertrophic cardiomyopathy, and, uncommonly, by congenital anomalies such as discrete subaortic stenosis. We describe a patient with Behcet's disease, presenting with a systolic murmur, fever, and syncope, in whom a diagnosis of subaortic obstruction caused by a pseudo-aneurysm dissecting the interventricular septum and associated with a complete atrioventricular block was made.- - - - - - - - - - ranking = 0.2keywords = stenosis (Clic here for more details about this article) |
10/13. Detection of discrete subaortic stenosis by 3-dimensional transesophageal echocardiography.We present a case with discrete subaortic stenosis diagnosed by 2D and 3D echocardiography. 3D echocardiography was useful to demonstrate its morphology and dynamic change of the left ventricular outflow tract area, providing important information for surgical intervention.- - - - - - - - - - ranking = 1keywords = stenosis (Clic here for more details about this article) |
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