1/32. Fine-needle aspiration cytology of esophageal leiomyomatosis.Leiomyomata are the most common benign neoplasms of the esophagus, but they are still very rare in comparison to malignant tumors of this organ. We report on the aspiration cytology findings of a case of esophageal leiomyomatosis in a 19-yr-old man. Diagn. Cytopathol. 1999;21:197-199.- - - - - - - - - - ranking = 1keywords = leiomyomatosis (Clic here for more details about this article) |
2/32. Imaging of diffuse esophageal leiomyomatosis: two case reports and review of the literature.Diffuse esophageal leiomyomatosis is a rare disorder which may be found in association with leiomyomas in other locations or with other disorders. We report two cases in men, one with associated tracheobronchial involvement, which illustrate the value of imaging in differentiating this entity from other causes of dysphagia and in establishing a diagnosis.- - - - - - - - - - ranking = 1keywords = leiomyomatosis (Clic here for more details about this article) |
3/32. Progressive esophageal leiomyomatosis with respiratory compromise.leiomyomatosis is a rare neoplastic condition of the pediatric esophagus. Presenting symptoms usually overlap with more common esophageal disorders, namely, gastroesophageal reflux. A patient is presented in whom leiomyomatosis progressed to the point of causing cachexia and respiratory compromise.- - - - - - - - - - ranking = 1keywords = leiomyomatosis (Clic here for more details about this article) |
4/32. Esophageal leiomyomatosis in a woman with a history of vulvar leiomyoma and Barrett's esophagus: a case report and review of the literature.BACKGROUND: The diagnosis and treatment of esophageal pathology remains a challenge despite advances in preoperative endoscopy, radiographic staging, and perioperative care. CASE REPORT: In this article, we present an interesting case of esophageal leiomyomatosis in a woman with a history of vulvar leiomyoma and Barrett's esophagus. This paper represents the first reported simultaneous occurrence of these three pathologic entities in the English literature. CONCLUSIONS: The clinical presentation and characteristic pathologic findings in patients with esophageal leiomyomatosis are reviewed. Diagnostic and therapeutic approaches to esophageal masses are discussed including the indications for esophageal resection.- - - - - - - - - - ranking = 1.2keywords = leiomyomatosis (Clic here for more details about this article) |
5/32. Diffuse leiomyomatosis of the esophagus.BACKGROUND: Leiomyomas are rare esophagus neoplasms. They are usually solitary, and the diffuse lesion is extremely rare. CASE REPORT: A 19-year-old male presented with a 3-year history of occasional dysphagia and postprandial regurgitation. The chest radiographs showed a huge mass in the posterior mediastinum. barium esophagograms showed narrowing of the middle third esophagus with proximal dilatation. The fibroesophagoscopy demonstrated multiple submucosal nodules below a level 22 cm from the incisor and covered with intact mucosa. CT scans of the chest showed a long segment of circumferential soft tissue in the posterior mediastinum which encircled and involved the upper two thirds of the esophagus. An intrathoracic esophagectomy with cervical esophagogastrostomy via the substernal route was performed. Grossly, multiple confluent myomatous nodules circumferentially involved the upper and middle third of the esophagus. Histologic findings showed diffuse leiomyomatosis of the esophagus. CONCLUSION: Esophageal leiomyomatosis should be considered in a young patient with long-standing dysphagia in whom smooth, tapered esophageal narrowing on barium study and circumferential esophageal wall thickening on CT scan are seen. An esophagectomy combined with a reconstruction procedure is indicated.- - - - - - - - - - ranking = 1.2keywords = leiomyomatosis (Clic here for more details about this article) |
6/32. Diffuse esophageal leiomyomatosis with localized dense eosinophilic infiltration.Diffuse esophageal leiomyomatosis is a rare cause of dysphagia. There is frequently a chronic inflammatory infiltrate, but here we present the first reported case in association with a dense infiltration of eosinophils and mast cells confined to the affected muscularis propria. This was successfully managed by long esophageal myotomy, with resolution of dysphagia and no symptomatic recurrence after 3 years.- - - - - - - - - - ranking = 1keywords = leiomyomatosis (Clic here for more details about this article) |
7/32. Imaging features of esophageal leiomyomatosis: a case report.Leiomyomas are the most common benign tumors of the esophagus. However, esophageal leiomyomatosis is a rare pathologic entity that has received little attention in the radiologic literature. We present a case of esophageal leiomyomatosis with imaging features on barium swallow and computed tomography (CT).- - - - - - - - - - ranking = 1.2keywords = leiomyomatosis (Clic here for more details about this article) |
8/32. The association of anorectal leiomyomatosis and diffuse oesophageal leiomyomatosis.Anorectal leiomyomatosis is exceedingly rare in children. Its association with the more common diffuse oesophageal leiomyomatosis has been documented in only two previous cases. This report describes the presentation, diagnosis and treatment of two further cases of diffuse oesophageal combined with anorectal leiomyomatosis.- - - - - - - - - - ranking = 2.2keywords = leiomyomatosis (Clic here for more details about this article) |
9/32. Alport syndrome and diffuse leiomyomatosis: deletions in the 5' end of the COL4A5 collagen gene.Alport syndrome (AS) is an hereditary glomerulonephritis that is mainly inherited as a dominant X-linked trait. Structural abnormalities in the type IV collagen alpha 5 chain gene (COL4A5), which maps to Xq22, have recently been detected in several patients with AS. The association of AS with diffuse esophageal leiomyomatosis (DL) has been reported in 24 patients, most of them also suffering from congenital cataract. The mode of transmission and the location of the gene(s) involved in this association have not been elucidated. Southern blotting using cDNA probes spanning the whole COL4A5 and a 5' end COL4A5 genomic probe showed that three out of three patients with the DL-AS association had a deletion in the 5' part of the COL4A5 gene extending beyond its 5' end. This indicates that the same gene, COL4A5, is involved in classical AS and in DL-AS and that the transmission of DL-AS is X-linked dominant. These results also suggest that leiomyomatosis might be due to the alteration of a second gene involved in smooth muscle cell proliferation, which is located upstream of the COL4A5 gene, and that there might be a contiguous gene deletion syndrome, involving at least the genes coding for congenital cataract, DL and AS.- - - - - - - - - - ranking = 1.2keywords = leiomyomatosis (Clic here for more details about this article) |
10/32. Esophageal leiomyomatosis.BACKGROUND: Esophageal leiomyomatosis is rare with an incidence that is essentially unknown with only a few reported cases. Characteristically there is proliferation of smooth muscle cells in the esophageal wall causing localized circumferential thickening. Esophageal leiomyomas are usually very slow growing and often asymptomatic. Symptomatic tumors are usually greater than five centimeters in diameter. The accepted treatment for esophageal leiomyomatosis has been surgical removal, which frequently requires esophagectomy with reconstruction. CASE REPORT: We report a case of a 29-year-old woman with esophageal leiomyomatosis whose presentation was not typical and magnetic resonance imaging proved diagnostic. This patient was effectively with enucleation of the tumor. CONCLUSIONS: Recommended treatment for this condition has been total esophagectomy with reconstruction, but we report a case treated with enucleation of the tumor.- - - - - - - - - - ranking = 1.4keywords = leiomyomatosis (Clic here for more details about this article) |
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