1/17. Intrascrotal rhabdomyosarcoma.rhabdomyosarcoma is the most frequent spermatic cord tumor of infants, children, and young adults, but also occurs as a primary tumor in the testis, epididumis, and testicular tunics. In the last fifteen years, 7 patients with intrascrotal rhabdomyosarcoma were treated at our institution, and an additional 155 cases were found on review of the English literature. On the basis of these 162 cases, incidence and survival statistics were calculated with particular attention to employed forms of therapy. An over-all survival of greater than 73 per cent should be obtainable with proper utilization of surgery, radiation therapy, and combination chemotherapy.- - - - - - - - - - ranking = 1keywords = rhabdomyosarcoma (Clic here for more details about this article) |
2/17. rhabdomyosarcoma of the spermatic cord. A case report with review of the literature.rhabdomyosarcoma is a rare malignant tumor that may occur in the spermatic cord in childhood. So far, 62 cases have been reported in the English literature. We describe a case of embryonal rhabdomyosarcoma of the spermatic cord in a 15-year-old boy, detailing clinical history, light microscopy, immunohistochemistry and treatment. In order to unquestionably demonstrate the myogenic differentiation of the neoplasm, it was decided to use a monoclonal antibody against MyoD1. The nuclear positivity of this phosphoprotein in the tumor cells confirmed the diagnosis of embryonal rhabdomyosarcoma. Consequently, the patient was treated with right radical orchiectomy and retroperitoneal lymph node dissection (RPLND). The latter is usually required because of the high incidence (more than 50% of cases) of positive retroperitoneal nodes, whereas subsequent adjuvant therapy is occasionally necessary. In the present case, we decided for a careful follow-up on the basis of the small size of the tumor and the absence of metastasis at diagnosis. The patient is alive and free of disease 12 months after surgery.- - - - - - - - - - ranking = 0.4keywords = rhabdomyosarcoma (Clic here for more details about this article) |
3/17. Paratesticular rhabdomyoma.A case of rhabdomyoma of the spermatic cord in an infant with cryptorchidism is reported. This extremely rare tumor has not been described in an extrascrotal position or at such a young age. Differential diagnosis includes malignant rhabdomyosarcoma. Although fetal-type rhabdomyoma of the head and neck generally is a benign tumor, the prognosis of paratesticular fetal-type rhabdomyoma is unknown. Long-term follow-up is recommended.- - - - - - - - - - ranking = 0.2keywords = rhabdomyosarcoma (Clic here for more details about this article) |
4/17. Primary rhabdomyosarcoma of the seminal vesicle.Sarcomas of the seminal vesicle are very rare and poorly documented; as it is not always possible to pinpoint a truly vesicular origin of the pelvic mass due to local spread at the time of presentation. The purpose of the article is to document and characterize a rhabdomyosarcoma of the seminal vesicle of which to the knowledge of the authors there has been no previous report in the English literature.- - - - - - - - - - ranking = 1keywords = rhabdomyosarcoma (Clic here for more details about this article) |
5/17. Ultrasound diagnosis of paratesticular rhabdomyosarcoma.rhabdomyosarcoma is the most common tumour of the lower genitourinary tract in children in the first two decades. Paratesticular rhabdomyosarcoma is associated with a significantly better outcome than lesions elsewhere in the genitourinary tract. Although ultrasound is considered the imaging modality of choice for evaluating intrascrotal pathology, the ultrasound appearance of paratesticular rhabdomyosarcoma has rarely been reported and may be confused with other disease entities such as epididymitis, adenomatoid tumour and leiomyoma. We present the ultrasound features of a paratesticular rhabdomyosarcoma, discussing the clinical features and differential diagnosis.- - - - - - - - - - ranking = 1.4keywords = rhabdomyosarcoma (Clic here for more details about this article) |
6/17. Thirty-year review of intrascrotal rhabdomyosarcoma.Between 1957 and 1987, 6 cases of intrascrotal rhabdomyosarcoma were found in the pathology records for northern ireland. Four of these tumours arose from paratesticular tissue and 2 were confined to the testis. Only 1 patient has died of his disease. Two were lost to follow-up after 21 years and are presumed cured. The remaining 3 remain alive and disease-free between 2 and 3 1/2 years after presentation.- - - - - - - - - - ranking = 1keywords = rhabdomyosarcoma (Clic here for more details about this article) |
7/17. Testicular carcinoma in situ associated with rhabdomyosarcoma of the spermatic cord.A 12-year-old boy had an embryonal rhabdomyosarcoma in the distal portion of the spermatic cord. The tumor partially surrounded the testis, infiltrated the testicular tunics and formed an intratesticular nodule near the rete testis. The unaffected testicular parenchyma exhibited the characteristic germ cells of carcinoma in situ. We describe an association between these 2 types of tumors.- - - - - - - - - - ranking = 1keywords = rhabdomyosarcoma (Clic here for more details about this article) |
8/17. Neurofibromatosis, factor ix deficiency, and rhabdomyosarcoma.A paratesticular rhabdomyosarcoma occurred in a child with factor ix deficiency and neurofibromatosis, illustrating the need to consider carefully the various etiologic possibilities of a soft-tissue mass in a child with neurofibromatosis and/or a bleeding disorder.- - - - - - - - - - ranking = 1keywords = rhabdomyosarcoma (Clic here for more details about this article) |
9/17. Fibrous hamartoma of infancy masquerading as a rhabdomyosarcoma of the spermatic cord.Fibrous hamartoma of infancy is an uncommon nonmalignant fibroproliferative tumor found predominantly in the upper torso within the first 2 years of life. We report a case of fibrous hamartoma of infancy, which presented as a rapidly growing scrotal mass clinically indistinguishable from a rhabdomyosarcoma of the spermatic cord. The clinical characteristics of this neoplasm as well as management are discussed.- - - - - - - - - - ranking = 1keywords = rhabdomyosarcoma (Clic here for more details about this article) |
10/17. Paratesticular rhabdomyosarcomas and leiomyosarcomas: a clinicopathological review.One case of embryonal paratesticular sarcoma and 2 cases of leiomyosarcomas are reported. The 13-year-old boy with embryonal sarcoma is well after an orchiectomy and high ligation of the spermatic cord followed by radiotherapy and chemotherapy. A 66-year-old man has been doing well after orchiectomy and hemiscrotectomy for a paratesticular leiomyosarcoma. The third patient had a highly pleomorphic leiomyosarcoma and died 2 months postoperatively. The clinical and histological diagnosis of paratesticular rhabdomyosarcomas and leiomyosarcomas is reviewed and the various therapeutic approaches to these neoplasms are discussed. Retroperitoneal lymph node dissection, radiotherapy and chemotherapy are important adjuncts to orchiectomy in the management of rhabdomyosarcomas. On the contrary, retroperitoneal lymph node dissection and radiotherapy are not indicated in leiomyosarcomas, since these neoplasms tend to metastasize by the hematogenous route and are radioresistant. At the present time we are unable to evaluate chemotherapy in the management of paratesticular leiomyosarcomas.- - - - - - - - - - ranking = 1.2keywords = rhabdomyosarcoma (Clic here for more details about this article) |
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