1/37. Isolated metastases of adenocarcinoma in the bilateral internal auditory meatuses mimicking neurofibromatosis type 2--case report.A 56-year-old male with a history of lung cancer presented with isolated metastases of adenocarcinoma in the bilateral internal auditory meatuses (IAMs), mimicking the bilateral acoustic schwannomas of neurofibromatosis type 2, and manifesting as rapidly worsening tinnitus and bilateral hearing loss. magnetic resonance imaging showed small tumors in both IAMs with no sign of leptomeningeal metastasis. The preoperative diagnosis was neurofibromatosis type 2. Both tumors were removed and the histological diagnoses were adenocarcinoma. neuroimaging differentiation of a solitary metastatic IAM tumor from a benign tumor is difficult, although rapidly progressive eighth cranial nerve dysfunction suggests a malignant process. Metastases should be considered as a rare diagnostic possibility in a patient with small tumors in both IAMs.- - - - - - - - - - ranking = 1keywords = hearing loss, hearing (Clic here for more details about this article) |
2/37. The neural correlates of 'deaf-hearing' in man: conscious sensory awareness enabled by attentional modulation.Attentional modulation of normal sensory processing has a two-fold impact on human brain activity: activation of a network of localized brain regions is associated with paying attention, and activation of specific sensory regions is enhanced relative to passive stimulation. The mechanisms underlying attentional modulation of perception in patients with lesions of sensory cortices are less well understood. Here we report a unique patient suffering from extensive bilateral destruction of the auditory cortices (including the primary auditory fields) who demonstrated conscious perception of the onset and offset of sounds only when selectively attending to the auditory modality. This is the first description of such an attentively modulated 'deaf-hearing' phenomenon and its neural correlates, using H(2)(15)O-PET. Increases in cerebral blood flow associated with conscious awareness of sound that was achieved by listening attentively (compared with identical auditory stimulation presented when the patient was inattentive) were found bilaterally in the lateral (pre)frontal cortices, the spared middle temporal cortices and the cerebellar hemispheres. We conclude that conscious awareness of sounds may be achieved in the absence of the primary auditory cortex, and that selective, 'top-down' attention, associated with prefrontal systems, exerts a crucial modulatory effect on auditory perception within the remaining auditory system.- - - - - - - - - - ranking = 2.4825238207301keywords = hearing (Clic here for more details about this article) |
3/37. First Croatian auditory brainstem implantation.A deaf female patient was diagnosed with bilateral acoustic neurinomas. diagnosis incorporated the standard audiological battery for sensorineural hearing loss, computed tomography and magnetic resonance imaging. The left side had been operated on four years previously in another clinic using the suboccipital approach. The auditory brainstem implant surgery was performed on the 'second side' using the same approach. It was an uneventful operation with good anatomy and no serious post-operative complications. Post-operatively, the patient performed exceptionally well, with up to 50 per cent of words recognized in the opened set and 85 per cent in the closed set, both without lip-reading.- - - - - - - - - - ranking = 1.0537749342596keywords = hearing loss, hearing, sensorineural hearing loss, sensorineural hearing, sensorineural (Clic here for more details about this article) |
4/37. First auditory brainstem implantation in poland: auditory perception results over 12 months.Auditory brainstem implants (ABIs) are a modern method of treatment of total bilateral deafness in cases of extracochlear origin. In most cases therapy is applied in patients with neurofibromatosis type 2 (NF2). This paper presents the results of surgical treatment and rehabilitation in a 28-year-old woman with bilateral, multiple tumours of the central nervous system causing total deafness. Simultaneous removal of the tumours and implantation of ABI allowed treatment of the potentially lethal pathology and hearing restoration. Improving auditory skills and excellent tests results were noted in the year following implantation.- - - - - - - - - - ranking = 0.49650476414602keywords = hearing (Clic here for more details about this article) |
5/37. Hearing restoration with auditory brainstem implants after radiosurgery for neurofibromatosis type 2.The auditory brainstem implant (ABI) is designed to restore useful auditory sensations in patients with neurofibromatosis Type 2 (NF2). The implantation is usually performed at the time of tumor removal in patients who do not undergo radiation treatment. The authors evaluated the performance of ABIs in three patients with NF2 in whom vestibular schwannoma continued to grow after radiation treatment. These three patients with NF2 received a 21-channel ABI; a translabyrinthine approach was used for both the tumor removal and the ABI placement. The interval between radiosurgery and the tumor removal plus device implantation ranged from 2 to 11 years. In all cases, the tumor was growing and the patients presented with total deafness. The mean number of active electrodes in these three patients was equivalent to the average results reported in other patients who received ABIs. The patients in this study used the ABI regularly for everyday life and obtained useful levels of environmental sound recognition. It is concluded that hearing function can be rehabilitated using ABIs in patients with NF2, even if radiosurgery fails to control the tumor growth.- - - - - - - - - - ranking = 0.49650476414602keywords = hearing (Clic here for more details about this article) |
6/37. Intraosseous dural arteriovenous fistula of the skull base associated with hearing loss. Case report.The most common clinical presentations of dural arteriovenous fistulas (DAVFs) are bruit, headache, increased intracranial pressure, and intracranial hemorrhage. In particular locations, such as the cavernous sinus or middle cranial fossa, cranial nerve involvement due to dural arterial steal or venous occlusion may develop. A case in which a DAVF is associated with hearing loss, however, has not previously been reported. The authors report a case in which an intraosseous DAVF and associated hearing loss probably resulted from cochlear nerve or vascular compression caused by the draining vein or nidus of the DAVF.- - - - - - - - - - ranking = 6keywords = hearing loss, hearing (Clic here for more details about this article) |
7/37. Central hearing loss with a bilateral inferior colliculus lesion.A case is presented of a 43-year-old man with bilateral lesions of the inferior colliculus (IC) due to central nervous system lymphoma. Our patient was found to have relatively normal pure-tone averages with severely reduced bilateral word recognition scores. This case illustrates that the presentation of a partial bilateral IC lesion may be of severely reduced word recognition accompanied by nearly normal pure-tone hearing.- - - - - - - - - - ranking = 4.496504764146keywords = hearing loss, hearing (Clic here for more details about this article) |
8/37. Cortical auditory disorder caused by bilateral strategic cerebral bleedings. Analysis of two cases.The authors present the anatomical and clinical features of cortical auditory dysfunction in two patients, in whom hypertensive bleedings destroyed the cortical auditory centres in both hemispheres. The second haemorrhage occurred four years after the first bleeding in both cases. The bleedings isolated the cortical hearing centres due to the destruction of the right and left temporal white matter. During the clinical course the symptomatology has changed in both patients: pure word deafness has transformed to cortical deafness and generalised auditory agnosia. Normal pattern of brain stem auditory evoked potentials suggested intact auditory pathways. Authors conclude that transformation of clinical forms of cortical auditory disorder can be explained by the tissue reaction to the subcortical bleeding in the cortical auditory centres.- - - - - - - - - - ranking = 0.49650476414602keywords = hearing (Clic here for more details about this article) |
9/37. Postoperative hearing recovery in a case of delayed hearing loss after acoustic neurinoma removal.Delayed postoperative hearing loss after acoustic neurinoma removal is seldom observed. The presented case illustrates the phenomenon of delayed postoperative hearing loss which was observed 4 days after removal of a large acoustic neurinoma. Intraoperative brainstem auditory evoked potentials (BAEP) revealed a gradual loss of wave V with preservation of wave I. In animal experiments a dissociated loss of BAEP has been associated with impairment of microcirculation due to secondary edema. Vasoactive treatment was initiated and after 11 days a partial hearing recovery could be documented. Transient disturbance in microcirculation of vasa nervorum of the cochlear nerve is assumed to be responsible for postoperative hearing fluctuation.- - - - - - - - - - ranking = 8.9790285848761keywords = hearing loss, hearing (Clic here for more details about this article) |
10/37. cochlear implantation in a Mandarin Chinese-speaking child with auditory neuropathy.Auditory neuropathy (AN) is a hearing disorder characterized by the preservation of outer hair cell function despite the absence of auditory brainstem responses. The pathophysiology and etiology of this condition remain unknown. Recent studies have shown that some patients with AN benefit significantly from cochlear implantation. These patients have all been native speakers of Western languages. A 3-year-old Mandarin-speaking boy was referred to our center because of speech delay. After a series of audiological surveys, retro-cochlear lesion was impressed. During the 2-year period of rehabilitation, poor speech discrimination out of proportion to aided hearing thresholds led to the diagnosis of auditory neuropathy. Because of the limited benefit from amplification, he received a cochlear implant. Significant improvement of speech perception skills assessed by a Mandarin auditory perception test was noted shortly after implantation. The post-implantation performance in this Mandarin-speaking child was consistent with that of reports for implantees speaking Western languages. For Mandarin-speaking children with AN who fail to benefit from conventional treatment, cochlear implantation may be a good alternative choice.- - - - - - - - - - ranking = 0.99300952829204keywords = hearing (Clic here for more details about this article) |
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