1/5. medullary sponge kidney associated with distal renal tubular acidosis in a 5-year-old girl.INTRODUCTION: medullary sponge kidney (MSK) is characterized by cystic dilatation of the inner medullary collecting ducts, which causes the kidneys to resemble a sponge. CASE REPORT: Although distal renal tubular acidosis (dRTA) is commonly observed in patients with MSK, we report a 5-year-old girl with MSK who had features of both dRTA (nephrocalcinosis, hypercalciuria, hypocitraturia) and proximal tubular dysfunction (hyperuricosuria, impaired tubular phosphate reabsorption and proteinuria). DISCUSSION: Metabolic acidosis, hypercalciuria, hypocitraturia, tubular phosphate reabsorption and growth retardation in the patient improved with alkali therapy.- - - - - - - - - - ranking = 1keywords = nephrocalcinosis (Clic here for more details about this article) |
2/5. Combined treatment of medullary sponge kidney by EDTA potassium citrate and extracorporeal shock wave lithotripsy.A case of successful renal calculus dissolution by the combined treatment which consists of irrigation with ethylenediaminetetraacetic acid (EDTA), potassium citrate, and extracorporeal shock-wave lithotripsy (ESWL) is described here. Renal irrigation via nephrostomy, which was the main treatment, was attempted on a 34-year-old Japanese male who had bilateral nephrocalcinosis caused by type 1 renal tubular acidosis associated with an impacted calculus in the right ureter. Finally, most of the calculi have been dissolved within 1 year.- - - - - - - - - - ranking = 1keywords = nephrocalcinosis (Clic here for more details about this article) |
3/5. medullary sponge kidney in childhood.medullary sponge kidney is reported in six children aged 2-18 years. One child was asymptomatic; the others had hematuria or a urine-concentrating defect. Renal function and size were otherwise normal, as was liver function. The diagnosis was made at excretory urography according to criteria established in adults. Sonography revealed hyperechogenic pyramids, at first at the periphery, later generalized. Computed tomography proved this to be calcium. medullary sponge kidney is rare but exists in children. Sonography is very sensitive to the pyramidal nephrocalcinosis that complicates this disease and explains the frequent presenting symptom of hematuria in these children.- - - - - - - - - - ranking = 1keywords = nephrocalcinosis (Clic here for more details about this article) |
4/5. A case of incomplete renal tubular acidosis (type 1) associated with medullary sponge kidney followed by nephrocalcinosis.A case is reported of incomplete renal tubular acidosis (type 1) associated with medullary sponge kidney followed by nephrocalcinosis. Although several cases of classic renal tubular acidosis associated with medullary sponge kidney have been documented a case of incomplete renal tubular acidosis associated with medullary sponge kidney seems to be rare. We recommend examination for incomplete renal tubular acidosis in patients with medullary sponge kidney and nephrocalcinosis without systemic acidosis.- - - - - - - - - - ranking = 6keywords = nephrocalcinosis (Clic here for more details about this article) |
5/5. medullary sponge kidney associated with congenital hemihypertrophy.medullary sponge kidney is a developmental disorder characterized by ectatic and cystic malformation of the collecting ducts and tubules. Clinical manifestations include urinary tract infections, renal stones, and hematuria. It can be associated with other developmental disorders. A case of medullary sponge kidney associated with congenital hemihypertrophy, complicated by nephrocalcinosis and nephrolithiasis, is reported here.- - - - - - - - - - ranking = 1keywords = nephrocalcinosis (Clic here for more details about this article) |