1/5. Nasal natural killer-cell lymphoma: a disease with very poor prognosis.Nasal Natural Killer-Cell lymphoma is an aggressive subtype of NHL even when it presents with localized disease. It is more common in Oriental than Western population. We report the case history of a white Caucasian male patient with this disease who died 5 months from diagnosis despite aggressive treatment with 2 different chemotherapy regimes and radiotherapy. We discuss the diagnosis, presentation, treatment and prognosis of this rare disease.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
2/5. Malignant triton tumor of the nasal cavity.BACKGROUND: Malignant triton tumor is usually an aggressive sarcoma consisting of a malignant schwannoma with rhabdomyoblastic differentiation. However, malignant triton tumor of the nasal cavity is very rare. methods: A case report of a 38-year-old woman with polypoid mass, which bled easily in the right nasal cavity, and nasal obstruction is presented with a review of the literature pertaining to this unusual case. RESULTS: The malignant triton tumor was treated with wide surgical excision followed by radiation therapy. Histopathological diagnosis of the malignant triton tumor was made on the surgical specimen. The patient's postoperative course was unremarkable, and follow-up at 5 years reveals no evidence of disease. CONCLUSIONS: A malignant triton tumor in the nasal cavity is a rare disease. head and neck surgeons should recognize the possibility of malignant triton tumor occurring in the nasal cavity.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
3/5. Sebaceous carcinoma of the nasal vestibule.Sebaceous carcinoma is a rare disease arising from holocrine adnexal components of the skin. Fewer than 400 cases have been reported worldwide and only about 19 are from the nose. We present a sebaceous cancer of the nasal vestibule in a patient who, with adequate excision, is disease-free after two years.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
4/5. Juvenile hyaline fibromatosis: a case report.Juvenile hyaline fibromatosis (JHF) is a rare disease with autosomal recessive inheritance. It is characterized by papulonodular skin lesions which are painless but cosmetically unacceptable, and often disturb normal joint function. The nose, chin, ears, scalp, back, and knees are the most common affected sites. In some cases, gingival hypertrophy, flexion contractures of the large joints, osteolytic bone lesions, and stunted growth may be associated with skin lesions. We report a 9-year-old girl presented with a soft, painless, slow growing, tumoral mass on the supratip of her nose. The lesion was totally excised with open rhinoplasty approach and histopathological diagnosis was JHF.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
5/5. Spheric mass beneath the alar base: MR images of nasolabial cyst and schwannoma.We report 2 cases of nasolabial cyst and a case of schwannoma beneath the alar base that required a differential diagnosis because of clinical features and MR images that resembled the nasolabial cyst. The morphologic analysis on MR images revealed the characteristic appearance of the nasolabial cyst, and the sagittal MR image may be most helpful for diagnosing this rare disease.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |