1/4. Post-traumatic osteolysis of the distal clavicle, pubis and ischium in 7 patients.Post-traumatic osteolysis (PTOL) is a very rare disease occurring after acute trauma or repetitive micro-trauma, which is characterized by persistent pain in the injured site. In this study, we reported 7 patients, in whom osteolysis developed in the distal clavicle, pubis and ischium.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
2/4. radiotherapy of Morbus Gorham-Stout: the biological value of low irradiation dose.Morbus Gorham-Stout is a very rare disease. A patient with this disease was treated at the University Clinic of radiobiology in Vienna. The clinical and radiological findings place special emphasis on the radiotherapeutic treatment, and the biological basis of the recommended dose is discussed.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
3/4. Massive osteolysis of the mandible.This report deals with a massive osteolysis, which is a rare disease characterized by the progressive dissolution of contiguous osseous structure, occurring in the mandible of a 46-year-old Japanese female. Histopathologic examination of the amputation material revealed that the mandibular body, ramus, condylar and coronoid processes were completely replaced by fibrous tissue, but inferior alveolar nerve and artery in the lesion were intact. A few small islands of osteoid tissue or immature fibrous bone were seen in the lesion. In the transitional area between the lesion and normal bone, active absorption of bone trabeculae was in progress and intertrabecular spaces were occupied by densely packed fibroblastic cells, however, angiomatous proliferation of vessels was not observed. A few bone trabeculae were surrounded by osteoclasts, but osteoclasts might not play a primary etiological role in massive osteolysis.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |
4/4. Congenital generalized fibromatosis: a case report with roentgen manifestations of the skeleton.Congenital generalized fibromatosis is a rare disease. Since the features were described in 1954, 23 cases have been mentioned in the literature. 4 cases that had been reported before that time may retrospectively be said to belong to this syndrome. Congenital generalized fibromatosis resembles clinically as well as roentgenologically neurofibromatosis and may therefore be classified as a hamartomatosis, although the histological distinction of the congenital fibrosarcoma may sometimes be difficult. In this case report, a young patient is described with clinical, roentgenological and histological features of congenital generalized fibromatosis.- - - - - - - - - - ranking = 1keywords = rare disease (Clic here for more details about this article) |