1/8. Calcipotriol treatment of confluent and reticulated papillomatosis (Gougerot-Carteaud syndrome).Gougerot-Carteaud syndrome or confluent and reticulated papillomatosis (CRP), was first described by Gougerot and Carteaud as dermatosis. It is generally considered a rare condition. The eruption consists confluent, flat, brown papules localized primarily to the intermammary and interscapular regions with subsequent spread to the breast and abdomen; at the periphery, the papules spread out forming a pigmented reticulated pattern. At present, the aetiology of CRP remains unknown. The two prominent theories are an abnormal host response to fungi and a keratinization defect. Other hypothesis include photosensitivity, genetic factor, amyloidosis cutis and endocrinopathy.- - - - - - - - - - ranking = 1keywords = dermatosis (Clic here for more details about this article) |
2/8. Confluent and reticulated papillomatosis of Gougerot and Carteaud.Confluent and reticulated papillomatosis is a rarely reported dermatosis of unknown origin. It is similar to nummular and confluent papillomatosis; punctate, pigmented verrucose papillomatosis; acanthosis nigricans; pseudoacanthosis nigricans; benign acanthosis nigricans; pseudoatrophoderma colli; tinea versicolor; Darier's disease; epidermodysplasia verruciformis; and verruca plana. Treatment may be temporarily successful, but the lesions usually recur within a period of months.- - - - - - - - - - ranking = 1keywords = dermatosis (Clic here for more details about this article) |
3/8. Confluent and reticulated papillomatosis (Gougerot-Carteaud) successfully treated with tacalcitol.Confluent and reticulated papillomatosis (CRP) is a rare dermatosis of unknown aetiology whose relationship to malassezia furfur is still debated. antifungal agents, antibiotics, retinoids, and, more recently, calcipotriol have been successfully used as treatment. The authors report on a 14-year-old female with confluent and reticulated papillomatosis in whom M. furfur was found. Anti-fungal therapy eliminated the fungus, but did not achieve the disappearance of the lesions. Further treatment with tacalcitol was successful, supporting the theory that CRP might be a disorder of keratinization. To the authors' knowledge, this is the first patient treated with tacalcitol for this entity.- - - - - - - - - - ranking = 1keywords = dermatosis (Clic here for more details about this article) |
4/8. Confluent and reticulated papillomatosis: response to tazarotene.Confluent and reticulated papillomatosis of Gougerot and Carteaud is an uncommon dermatosis of unclear cause that can be recalcitrant to therapy. We report the case of an 11-year-old black girl with the eruption in whom it completely cleared using tazarotene gel. The treatment was well-tolerated and we suggest considering topical tazarotene as an alternative to systemic retinoid therapy.- - - - - - - - - - ranking = 1keywords = dermatosis (Clic here for more details about this article) |
5/8. Three cases of focal dermal hypoplasia (Goltz syndrome).focal dermal hypoplasia or Goltz syndrome is a rare genodermatosis, characterized by multiple abnormalities of ectodermal and mesodermal origin. It is found predominantly in females and is characterized by hypoplasia of skin and papillomas. Three cases of focal dermal hypoplasia in infancy with unusual inheritance patterns are reported. Cutaneous features were atrophic reticulated scars involving the trunk and extremities following the lines of Blaschko. Papillomas were present on the genitalia and in a periorificial distribution. Skeletal abnormalities included syndactyly, polydactyly and lobster claw deformities. Ophthalmological examination revealed strabismus and retinal colobomas.- - - - - - - - - - ranking = 1keywords = dermatosis (Clic here for more details about this article) |
6/8. Cowden's syndrome. Case report, with reference to an affected family.Cowden's syndrome is a rare genodermatosis characterized by multiple hamartomas in several tissues and organs derived from all three embryonic layers. Clinical features of Cowden's disease are explained by the mutation of the PTEN tumour suppressor gene, whose modification leads to an uncoordinated growth of tissues. The importance of this disease lies in the increased susceptibility to malignization of some lesions, specially breast, thyroid and genito-urinary tract lesions. As a result, the disease has been considered a preneoplasic condition. Despite its varied phenotypic expression, this disease is generally unknown. Consequently, many cases are undiagnosed or diagnosis comes at a late stage, what points out the importance of an early diagnosis of the disease so the patient can have periodic check-ups to prevent malignant diseases. A family case is presented here, whose diagnosis was based upon oral clinical findings and which most distinct systemic alteration is the presence of hamartomatous polyps in the digestive tract in several family members.- - - - - - - - - - ranking = 1keywords = dermatosis (Clic here for more details about this article) |
7/8. A case of early onset confluent and reticulated papillomatosis with an unusual localization.Confluent and reticulated papillomatosis is a relatively rare dermatosis of unknown origin. It is characterized by papules that become confluent in the center and reticulated at the periphery. The sites of predilection are the neck, interscapular region, inframammary area and abdomen. In a 15-year-old girl diagnosed with confluent and reticulated papillomatosis, the lesions first appeared on her knees and elbows when she was 4-years-old, and on the interscapular area when she was 13. Similar lesions arose on the left hand a few weeks previous to her visit. Two biopsy specimens were taken from the interscapular and elbow areas. The histopathological findings of this case fit the diagnosis of confluent and reticulated papillomatosis. We expect good results from azithromycin therapy.- - - - - - - - - - ranking = 1keywords = dermatosis (Clic here for more details about this article) |
8/8. Multiple hamartoma syndrome presenting with oral lesions.Multiple hamartoma syndrome (Cowden's syndrome), a rare genodermatosis with predominant mucocutaneous features, particularly hamartomas, and Cowden/Lhermitte-Duclos disease, the combination of multiple hamartomas with cerebellar hypertrophy, typically present with cutaneous and oral papillomatosis as major features of both uncommon disorders. This article details the clinical features of three patients with multiple hamartoma syndrome and one with both disorders.- - - - - - - - - - ranking = 1keywords = dermatosis (Clic here for more details about this article) |