1/41. Progressive pedal macrodactyly surgical history with 15 year follow-up.Macrodactyly can affect the fingers and/or toes1. Histopathologic examination will distinguish macrodactylia fibrolipomatosis or neural fibrolipoma with macrodactyly, from macrodactylia as a part of neurofibromatosis. Surgical repair is aimed at decreasing the size of the affected foot so it is as near in size and shape to the normal foot as possible. Surgical approaches have included reconstructive surgery (usually staged debulking procedures), epiphyseal plate arrest and amputation. Repeated reconstructive surgical procedures, as illustrated in this report covering patient care over a 15 year period, are usually necessary due to recurring soft tissue and boney enlargement.- - - - - - - - - - ranking = 1keywords = fibromatosis (Clic here for more details about this article) |
2/41. Fibromatosis mimicking clinically invasive breast carcinoma.Our purpose is to report two cases of fibromatosis in two women of 34 and 48 years old respectively that clinically appeared as a invasive breast carcinoma, particularly for the cutaneous retraction they showed. The histopathological diagnosis was done based on specimens studied with the common technique of paraffin embedding and Hematoxilin & Eosin staining. Both patients had firm poorly demarcated nodules with the histopathological pattern of classic fibromatosis. Mammary fibromatosis is an infrequent relapsing entity, not suspected in differential clinical diagnoses. The pathologist should bear it in mind, especially in frozen biopsies.- - - - - - - - - - ranking = 3keywords = fibromatosis (Clic here for more details about this article) |
3/41. Recurrent massive subperiosteal hematoma in a patient with neurofibromatosis.The authors report the case of a 13-year-old neurofibromatosis (NF-I) patient who suffered a blunt trauma in 1993. The diagnosis of subperiosteal hematoma was made. The pathogenesis of subperiosteal hematoma is discussed.- - - - - - - - - - ranking = 5keywords = fibromatosis (Clic here for more details about this article) |
4/41. Hereditary gingival fibromatosis: report of three cases.Three cases of generalized and severe HGF in young patients of the same family without other features are reported. The purpose of this article is to present documented cases and discuss the identification, treatment, and control of the disease. The histopathological characteristics of HGF are emphasized.- - - - - - - - - - ranking = 4keywords = fibromatosis (Clic here for more details about this article) |
5/41. Neurofibromatosis, gigantism, elephantiasis neuromatosa and recurrent massive subperiosteal hematoma: a new case report and review of 7 case reports from the literature.The authors report the case of a 13-year-old patient with neurofibromatosis (NF-I), who suffered blunt trauma to the left tibia in 1993. The diagnosis of subperiosteal hematoma was made. Treatment consisted of temporary rest. There was a recurrence in 1996, and the subperiosteal hematoma was drained. In 1997, a shortening osteotomy of the left tibia was performed. However, massive gigantism with elephantiasis of the left leg remained, causing a serious functional and cosmetic problem. In 1999, the leg was amputated above the knee. The literature is reviewed and 7 case reports are compared. The pathogenesis of subperiosteal hematoma is discussed.- - - - - - - - - - ranking = 5keywords = fibromatosis (Clic here for more details about this article) |
6/41. Recurrent pyogenic meningitis: an unusual presentation in a case of neurofibromatosis-1.We report a case of recurrent pyogenic meningitis with cerebrospinal fluid rhinorrhoea in a patient with neurofibromatosis-1, which has not been reported previously.- - - - - - - - - - ranking = 5keywords = fibromatosis (Clic here for more details about this article) |
7/41. Recurrent infantile digital fibromatosis--a rare entity.We present here a rare case of Infantile Digital Fibromatosis in a six year old female child who presented with recurrent swelling over the phalanx of left middle finger.- - - - - - - - - - ranking = 4keywords = fibromatosis (Clic here for more details about this article) |
8/41. Neurofibromatosis type 2--the importance of serial imaging of the brain and spinal cord.Meningiomas and schwannomas are relatively common central nervous system neoplasms, but patients harbouring multiple meningiomas or schwannomas are rare. We present the case of a 27 year-old patient with Neurofibromatosis type 2 with multiple associated intracranial meningiomas and spinal cord neurofibromas at various levels. patients with Neurofibromatosis type 2 should be followed up for life with serial magnetic resonance imaging of the brain and spinal cord to detect new and recurrent tumours at these sites.- - - - - - - - - - ranking = 6keywords = fibromatosis (Clic here for more details about this article) |
9/41. Schwannomatosis in a child--or early neurofibromatosis type 2.A case of multiple cervical schwannomas in a five-year-old boy, without other evidence of neurofibromatosis type 2, is described. Schwannomatosis is a disorder characterized by the presence of multiple schwannomas in the absence of neurofibromatosis type 2 that has only been recognized in the last 15 years. The clinical and genetic features of neurofibromatosis types 1 and 2 and schwannomatosis are compared and contrasted. This patient with possible schwannomatosis is presented to illustrate the potential pitfalls of making this diagnosis in the paediatric age group and to increase awareness of the debate on whether this is a distinct entity or a form fruste of neurofibromatosis type 2.- - - - - - - - - - ranking = 8keywords = fibromatosis (Clic here for more details about this article) |
10/41. Hereditary gingival fibromatosis: a case report.BACKGROUND/AIMS: Hereditary gingival fibromatosis is characterized by various degrees of attached gingival overgrowth. It usually develops as an isolated disorder but can be one feature of a syndrome. A case of a 38-year-old female is reported who presented a generalized severe gingival overgrowth, involving the maxillary and mandibular arches and covering almost all teeth. The clinical differential diagnosis included drug-induced overgrowth as well as idiopathic gingival fibromatosis. TREATMENT: Excess gingival tissue was removed by conventional gingivectomy. As the gingival enlargement was generalized to all quadrants, on both sides, the surgery was carried out under general anaesthesia. The postoperative course was uneventful and the patient's appearance improved considerably. Post-surgical follow-up after 20 months demonstrated a slight recurrence CONCLUSIONS: Hereditary gingival fibromatosis is a rare disorder characterized by the proliferative fibrous overgrowth of the gingival tissue. Resective surgery of the excess tissue is the treatment available. However, recurrence is a common feature.- - - - - - - - - - ranking = 7keywords = fibromatosis (Clic here for more details about this article) |
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