1/7. Ruptured giant intrathoracic lipoblastoma in a 4-month-old infant: CT and MR findings.BACKGROUND: We describe a 4-month-old infant with a ruptured intrathoracic lipoblastoma arising from the parietal pleura and associated with a pleural effusion. OBJECTIVE: The clinical presentation was rapidly evolving respiratory distress. The chest radiograph showed a large mass and a pleural effusion in the right thoracic cavity. CT demonstrated an inhomogeneous low-attenuation mass which was 7 cm in diameter and which showed areas of enhancement after intravenous contrast medium. MRI showed a fatty intrathoracic mass with intratumoral streaks and whorls, which were attributed to loose fibrovascular connective tissue on pathological examination. RESULTS: thoracotomy and pathological examination revealed a ruptured intrathoracic lipoblastoma arising from the parietal pleura. CONCLUSION: The pleural effusion might have suggested rupture of the tumour.- - - - - - - - - - ranking = 1keywords = lipoblastoma (Clic here for more details about this article) |
2/7. thoracic wall lipoblastoma: a case report and review of histopathology and cytogenetics.A rare case of a successfully excised intra- and extrathoracic lipoblastoma of the anterior chest wall in a 13-month-old female infant is reported. Histopathology and cytogenetical analysis established the diagnosis of a lipoblastoma. The differential diagnosis, histology and cytogenetical evaluation of lipomatous neoplasms are discussed. Karyotypic analysis may be of use in diagnostically difficult cases owing to the characteristic alterations in 18q11-13. A complete resection of lipoblastomas is feasible and advantageous with no need for a mutilating radical excision.- - - - - - - - - - ranking = 1.1666666666667keywords = lipoblastoma (Clic here for more details about this article) |
3/7. lipoblastoma: better termed infantile lipoma?lipoblastoma is a rare adipose tumor occurring exclusively in childhood. There have been no reports of metastases, making the designation "blastoma" confusing, since this term is usually reserved for malignant tumors. Two recent cases treated at our institution confirm its benign nature. In addition, a review of the literature supports the idea that the tumor may more accurately be described as an "infantile lipoma". Infantile lipoma better reflects many of the tumor's characteristics such as, its early occurrence, it's ability to mature into a simple lipoma, it's cellular composition of mainly mature adipocytes, and its benign course. Although lipoblastoma is an uncommonly encountered tumor, making an effort to change its name to infantile lipoma will result in a more a accurate term that will facilitate treatment.- - - - - - - - - - ranking = 0.16666666666667keywords = lipoblastoma (Clic here for more details about this article) |
4/7. Benign chest wall lipoblastoma: report of a case.This report deals with a 22-month-old boy who had a benign lipoblastoma on the chest wall. The tumor was located intrathoracically and was well-encapsulated. It was yellowish in color with a shiny cut surface and consisted of multiple lobules. Histologically, peripheral immature lipoblasts with fat vacuoles of various size and central mature fat cells containing a single, large fat vacuole are characteristic of this tumor. No local recurrence has been found during the 17 months since total excision.- - - - - - - - - - ranking = 0.83333333333333keywords = lipoblastoma (Clic here for more details about this article) |
5/7. lipoblastoma in infants and children.lipoblastoma and lipoblastomatosis are rare benign tumors of embryonal fat with a tendency to local invasion but not to metastasize. To date, there have been 60 cases described in the international literature. There has never been a report in a child older than 8 yr. The main clinical characteristics are the presentation, usually below 3 yr of age, the rapid growth of the mass and the peripheral location, mainly in the extremities. Although CT scan may show a fatty tumor, there is no single test to make the differential diagnosis (which includes benign lipoma, liposarcoma and myxoliposarcoma) and the treatment should be based on clinical findings. We have treated four patients with this condition. Two were intrathoracic, one was intraperitoneal, and one was a tumor of the upper arm. All presented as rapidly-growing tumors and were clinically assumed to be malignant. We recommend complete but conservative excision of the tumor; there are reported recurrences after inadequate excision. This is a benign tumor and radical cancer surgery should be avoided.- - - - - - - - - - ranking = 0.16666666666667keywords = lipoblastoma (Clic here for more details about this article) |
6/7. Benign chest wall lipoblastoma of infancy producing underlying bone enlargement.We report a case of a chest wall lipoblastoma first presenting in a 6-month-old infant. Clinical presentation was with a posterior chest wall mass. Chest X-ray showed expansion of the posterior ribs on the left, a feature not previously described in this condition. CT scanning delineated a mass of predominantly fat attenuation, which was invading between the ribs to line the extra-pleural space, and was causing compression and atrophy of muscles locally. There were two recurrences requiring further surgery. histology showed a well-differentiated lipoblastoma.- - - - - - - - - - ranking = 1keywords = lipoblastoma (Clic here for more details about this article) |
7/7. Lipoblastomatosis in a newborn: case report.A male newborn had a well-circumscribed, solid mass on the right anterior chest wall at birth. Computed tomography disclosed an infiltrating soft-tissue mass over the right 6th to 9th ribs near the costochondral junction. Surgical excision was done at the age of 5 days. Pathologic examination showed lipoblastomatosis.- - - - - - - - - - ranking = 0.16666666666667keywords = lipoblastoma (Clic here for more details about this article) |