| A case of an association of extrahepatic biliary atresia (EHBA) and urogenital sinus (UGS) anomaly that was diagnosed as an urachal remnant antenatally is reported. Diagnostic laparoscopy of the abdominal cavity in the postnatal period was the most helpful step for making the diagnosis. biliary atresia and urogenital sinus, which was the cause of bladder outlet obstruction, were treated successfully. To the authors' knowledge, this is the first case of this type of association introduced to the literature. J Pediatr Surg 36:635-637. ( info) |
12/161. Inverted papilloma of bladder. The fifth reported case of a rare variant of transitional papillary tumor of the bladder termed inverted papilloma is reported with a brief review of the literature. This tumor is likely to be confused with invasive malignant papillary carcinoma although it has adistinct histologic pattern, and it is for this reason that attention is drawn to the entity. ( info) |
13/161. Cystic rectal duplication: a rare cause of neonatal bladder-outlet obstruction and hydronephrosis. A case of cystic rectal duplication (RD) is presented. A 7-day-old female was admitted with acute urinary retention, voiding difficulty, and abdominal distention since she was 4 days of age. Ultrasound and abdominal computed tomography (CT) demonstrated a huge, cystic mass in the pelvis and abdomen that resulted in acute urinary retention and bilateral hydronephrosis. CT-guided drainage of the lesion followed by transabdominal surgical excision resulted in a cure. Pathologic examination demonstrated a RD lined by respiratory epithelium. ( info) |
14/161. Prenatal sonographic diagnosis of bladder outlet obstruction caused by a ureterocele associated with hydrocolpos and imperforate hymen. We report a case of prenatal bladder obstruction due to a single system ureterocele associated with hydrocolpos. Ultrasound at 22 weeks demonstrated an enlarged bladder. Serial scans showed progressive ipsilateral obstructive uropathy, contralateral hydronephrosis, and oligohydramnios. Neonatal endoscopic decompression and hymenotomy was performed with residual decreased ipsilateral renal function and dilation. Prenatal bladder obstruction may cause permanent renal damage. ( info) |
15/161. Left multicystic dysplastic kidney with contralateral ectopic kidney and ureterovesicle junction obstruction. multicystic dysplastic kidney (MCDK) represents the most common cause of abdominal mass in the neonatal period. It is usually combined with contralateral genitourinary tract anomaly. Because the multicystic dysplastic kidney is usually dysfunctional, it is important to evaluate and monitor the remaining preserved function of the contralateral kidney regularly. The presence of severe obstructive lesion over contralateral kidney is often life-threatening. Prompt treatment should therefore be given as early as possible to preserve the remaining renal function. We here report one rare case of left MCDK with contralateral ectopic kidney and ureterovesicle junction (UVJ) obstruction. As the best as we know, this report is the first case report of MCDK with contralateral ectopic kidney and UVJ obstruction. ( info) |
16/161. In utero intervention in a patient with prune-belly syndrome and severe urethral hypoplasia. Prenatal ultrasound scanning of a 20-year-old woman at 17 weeks of gestation revealed findings suggestive of bladder outlet obstruction, including bladder distension, dilated bilateral ureters, urinary ascites, and oligohydramnios. Vesicoamniotic shunts were placed with decompression of the bladder and correction of the amniotic fluid levels. Labor was induced at 36 weeks' gestation. At birth, the infant was noted to have prune-belly syndrome with severe urethral hypoplasia, a variant usually associated with a poor prognosis, necessitating vesicostomy for bladder drainage. We present a case of a patient with prune-belly syndrome and bladder outlet obstruction in whom early intervention resulted in an excellent outcome with preservation of renal and pulmonary function. ( info) |
17/161. In-utero treatment of fetal bladder-outlet obstruction by a ureterocele. Fetal bladder-outlet obstruction by ureteroceles is usually treated at birth. However, such obstruction may be detrimental to the health of the fetus and so in-utero correction is preferable. We describe the successful cytoscopy guided laser incision, with no complications, of a uterocele that was causing bladder-outlet obstruction in a fetus of 19 weeks and 6 days gestation. ( info) |
18/161. Normal paraganglia in the human prostate. A normal paraganglion was discovered incidentally in prostatic fragments resected for nodular prostatic hyperplasia. ( info) |
19/161. Endoscopic treatment of complete bladder neck obstruction by transurethral Seldinger technique. Bladder neck contracture is usually a complication of prostatectomy and the treatment of choice in such a condition should be endoscopic surgery. However, in a few patients the bladder neck may be completely obstructed preventing retrograde access into the bladder. A case is presented of complete bladder neck obstruction occurring after transurethral resection of prostate, which was treated after an access was provided by using transurethral Seldinger technique. ( info) |
20/161. Ureteral pressure flow studies in difficult diagnostic problems. Before a ureteral operation is undertaken for dilated, non-refluxing ureters it is essential to determine whether obstruction is present, since an operation is unnecessary and can be hazardous if there is no obstruction or infection. Obstruction is most accurately diagnosed by perfusing the upper tract at a known flow rate and measuring the resulting pressure. This test was performed on 5 patients in whom there was doubt as to the presence of obstruction from the radiographic evidence. In 4 of the 5 patients low pressure was found, the obstruction was excluded and an operation was avoided. In the fifth patient the obstruction was confirmed and relieved. The pressure flow test is useful in the diagnosis or exclusion of obstruction in the upper urinary tract. ( info) |