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Symptoms:
Propionic Acidemia; Glycinemia, Ketotic; Ketotic Glycinemia; Ketotic Hyperglycinemia; PCC Deficiency; Propionicacidemia; Propionyl-CoA Carboxylase Deficiency
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More information
propionic acidemia
Active principles
Rating
Bibliogr.
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1
Carboxy-Lyases
100
+
2
Methylmalonyl-CoA Decarboxylase
95
+
3
Propionates
44
+
4
Biotin
43
+
5
Ligases
34
+
6
Pyruvate Carboxylase
34
+
7
Carbon-Carbon Ligases
22
+
8
Glycine
12
+
9
Sodium Benzoate
11
+
10
Carbon-Nitrogen Ligases
11
+
11
Strychnine
10
+
12
Acetyl-CoA Carboxylase
10
+
13
Malonates
10
+
14
Biotinidase
8
+
15
Benzoic Acid
8
+
16
Hexosediphosphates
8
+
17
Crotonates
8
+
18
Methylmalonic Acid
8
+
19
Ketone Bodies
7
+
20
Glycine Dehydrogenase (Decarboxylating)
7
+
21
Hydroxybutyrates
6
+
22
Acetoacetates
6
+
23
Dextromethorphan
6
+
24
Valerates
6
+
25
Phosphofructokinase-2
5
+
26
Transferases
5
+
27
Heptanoates
5
+
28
Apoenzymes
5
+
29
Ammonia
5
+
30
Acyl Coenzyme A
4
+
31
3-Hydroxybutyric Acid
4
+
32
Receptors, Glycine
3
+
33
Methylmalonyl-CoA Mutase
3
+
34
Carnitine
3
+
35
Amidohydrolases
3
+
36
Pentanoic Acids
3
+
37
Isovaleryl-CoA Dehydrogenase
3
+
38
Benzoates
2
+
39
Oxidoreductases Acting on CH-CH Group Donors
2
+
40
Blood Glucose
2
+
41
Insulin
2
+
42
Ribulose-Bisphosphate Carboxylase
1
+
43
Blood Coagulation Factors
1
+
44
Acetyl Coenzyme A
1
+
45
Receptors, AMPA
1
+
46
Glutarates
1
+
47
alpha-Amino-3-hydroxy-5-methyl-4-isoxazolepropionic Acid
1
+
48
Fatty Acid Synthases
1
+
49
Isocoumarins
1
+
50
Formates
1
+
51
Fatty Acids, Volatile
1
+
52
Vitamin B 12
1
+
53
Hydroxocobalamin
1
+
54
Malonyl Coenzyme A
1
+
55
Iron
1
+
56
AMP-Activated Protein Kinases
1
+
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