1/6. Paratesticular fibrous pseudotumor in a patient with Gorlin's syndrome: nevoid basal cell carcinoma syndrome.An 18-year-old man with Gorlin's syndrome (the nevoid basal cell carcinoma syndrome) underwent excisional biopsy of a fibrous pseudotumor of the tunica vaginalis. Preoperative ultrasound confirmed the extraparenchymal nature of this paratesticular lesion, permitting a transscrotal approach. The pathophysiological considerations suggest that this finding (to our knowledge the first such case reported in association with Gorlin's syndrome) may be more than coincidental.- - - - - - - - - - ranking = 1keywords = tunica (Clic here for more details about this article) |
2/6. nephrogenic fibrosing dermopathy/nephrogenic systemic fibrosis: report of a new case with literature review.nephrogenic fibrosing dermopathy (NFD) is a fibrosing condition of the skin that is being described increasingly in patients with renal diseases, many of whom are on dialysis therapy or have undergone renal transplantation. Its etiopathology is unknown, and no standard therapy currently exists. We describe a patient with NFD for whom histopathologic studies indicated that the fibrotic process affected subcutaneous tissue, striated muscles, diaphragm, pleura, pericardium, great vessels of the heart, left ventricle and septum, and tunica albuginea in addition to the dermis. Fibroblast-like cells positive for CD34 and CD45RO and scattered CD68-positive cells were found in affected tissues. The presentation of our case is unusual in that the disease process started in the lower abdomen and upper extremities and involved the upper extremities to a greater extent than the lower extremities. Our findings indicate that the fibrosis associated with NFD can extend beyond dermis and, as part of a systemic fibrosing disorder, can involve subcutaneous tissues, striated muscles, diaphragm, pleura, pericardium, and myocardium. We therefore suggest that "nephrogenic systemic fibrosis" would be a more appropriate term for this disease entity.- - - - - - - - - - ranking = 1keywords = tunica (Clic here for more details about this article) |
3/6. Fibromatous periorchitis of testis.Fibrous pseudotumors of the tunica vaginalis, epididymis, and spermatic cord are uncommon benign paratesticular masses. An extremely rare variant termed "fibromatous periorchitis" exhibits diffuse proliferative encasement of the testis and manifests grossly as an indurated testis reminiscent of malignancy. We present the case of a 25-year-old man who presented with a grossly abnormal testicular examination and benign scrotal ultrasound findings and pathologic evidence of fibromatous periorchitis. The natural history, gross and histologic findings, and management of fibrous pseudotumors and fibromatous periorchitis are discussed.- - - - - - - - - - ranking = 1keywords = tunica (Clic here for more details about this article) |
4/6. fibrosis of tunica albuginea: complication of long-term intracavernous pharmacological self-injection.We report 3 cases of penile curvature deformity and fibrosis of the tunica albuginea after long-term self-injection with papaverine hydrochloride and phentolamine mesylate. To our knowledge this complication has not been reported previously. The clinical presentation and possible etiology are discussed.- - - - - - - - - - ranking = 5keywords = tunica (Clic here for more details about this article) |
5/6. Fibrous pseudotumor of the tunica vaginalis testis: imaging appearance.Fibrous pseudotumor is a benign paratesticular tumor that typically presents as a painless mass of the hemiscrotum. Because this tumor can mimic a malignant process, it is usually not diagnosed preoperatively. We describe a case of fibrous pseudotumor of the tunica vaginalis, demonstrating the ultrasound and magnetic resonance image (MRI) appearance with pathologic correlation.- - - - - - - - - - ranking = 5keywords = tunica (Clic here for more details about this article) |
6/6. Corporeal fibrosis as a result of priapism prohibiting function of self-contained inflatable penile prosthesis.Corporeal fibrosis and erectile impotence are known sequelae of priapism. fibrosis following priapism may make subsequent placement of a penile prosthesis, especially inflatable devices, difficult or impossible. A case is described in which a self-contained inflatable prosthesis (Dynaflex) was successfully placed to treat impotence resulting from idiopathic priapism. However, fibrosis of the distal tunica albuginea of the corpora cavernosa rendered them noncompressible, and thus precluded inflation of the device with its distally placed pump mechanism. This anatomic problem is added to the list of potential contraindications to placement of self-contained inflatable penile prostheses, and the advisability of having patients who desire such a prosthesis also choose a secondary prosthesis type is emphasized.- - - - - - - - - - ranking = 1keywords = tunica (Clic here for more details about this article) |