1/128. Congenital hernia of the abdominal wall: a differential diagnosis of fetal abdominal wall defects.A 28-year-old woman was referred at 33 weeks of gestation with suspected fetal intestinal atresia. Sonography showed a large extra-abdominal mass on the right of the normal umbilical cord insertion. Following cesarean section at 36 weeks and immediate surgical treatment, the malformation was not definable either as an omphalocele or as gastroschisis. This reported case involves a previously undocumented malformation of the fetal abdominal wall described as a 'hernia' of the fetal abdominal wall.- - - - - - - - - - ranking = 1keywords = defect (Clic here for more details about this article) |
2/128. OEIS complex (omphalocele-exstrophy-imperforate anus-spinal defects) in monozygotic twins.The omphalocele-exstrophy-imperforate anus-spinal defects (OEIS) complex is a consistent and recognizable pattern of midline abdominal and pelvic defects. It is rare, affecting 1 in 200,000 to 400,000 pregnancies and is even rarer in twin gestations. This is an autopsy study of OEIS complex in monozygotic twins after pregnancy termination at 20 weeks of gestation. Unremarkable family history but concordance of monozygotic twins for the defects may support the theory that early malformation complexes, e.g., OEIS, and monozygotic twinning are manifestations of the same disturbance of early blastogenesis.- - - - - - - - - - ranking = 1.75keywords = defect (Clic here for more details about this article) |
3/128. Terminal transverse limb defects with tethering and omphalocele in a 17 week fetus following first trimester misoprostol exposure.We report a fetus from an elective termination at 17 weeks gestation following maternal ingestion of 1200 micrograms of misoprostol at 7 weeks of gestation. The fetus had abscence of the middle and distal phalanges of fingers 1, 3, 4 and 5 with tethering by thin strands of tissue on one hand, a below-knee amputation of one leg and omphalocele. There was absence of amnion on the chorionic surface of the placenta, a pathologic feature of early amnion rupture. The association in this case of the phenotypic features of the amniotic band syndrome suggests that the teratogenicity of misoprostol at 9 to 12 weeks gestation can overlap that of other acute insults at that time, such as chorionic villus sampling, dilatation and curettage and abdominal trauma in the first trimester.- - - - - - - - - - ranking = 1keywords = defect (Clic here for more details about this article) |
4/128. prenatal diagnosis of complicated abdominal wall defects.The accurate prenatal diagnosis of anterior abdominal wall defects is important because it affects patient management and prognosis. The pathophysiology of each defect leads to key characteristics that make it possible to differentiate one entity from another. Among these features are the location of the defect in relation to cord insertion, the size and contents of the defect, and the associated anomalies. This article reviews the underlying defects, the characteristic ultrasound findings, the associated anomalies, and the prognosis of simple and complicated abdominal wall defects. The basic features of simple abdominal wall defects (i.e., omphalocele and gastroschisis) were used as the initial points of assessment. A comparison of the different features of these abnormalities and how they differ from one another resulted in the development of criteria that facilitated the understanding of the different ultrasound manifestations of these anomalies.- - - - - - - - - - ranking = 2.75keywords = defect (Clic here for more details about this article) |
5/128. A case with Weaver syndrome operated for congenital cardiac defect.An 11-month-old Turkish female infant with Weaver syndrome together with atrial septal defect and patent ductus arteriosus which was operated successfully is reported. Weaver syndrome is a very rare disorder of unknown etiology characterized by accelerated growth of prenatal onset, advanced osseous maturation, special craniofacial features, umbilical hernia, and hoarse low-pitched cry. Congenital cardiac defect is not a usual finding. The presented case is the first reported child with Weaver syndrome in the literature operated for a congenital cardiac defect.- - - - - - - - - - ranking = 2.4381393794342keywords = septal defect, defect, atrial septal defect (Clic here for more details about this article) |
6/128. heart block after induction of anesthesia in a child.A case of complete heart block occurred after induction of halothane anesthesia in a previously healthy child. The patient underwent repair of an umbilical hernia under general anesthesia. After a standard halothane, nitrous oxide, and oxygen mask induction, complete heart block was noted on the electrocardiographic monitor. atropine and 100% oxygen were administered, and sinus tachycardia resulted. With the immediate stabilization of the patient's condition, the surgical team agreed to proceed with the case. After deepening of the level of anesthesia, first with halothane and then with desflurane and easy intubation of the trachea, complete heart block again was noted. oxygen was administered at 100%, sinus tachycardia resumed, the case was canceled, and the patient emerged from anesthesia without further incident. The patient had an uneventful recovery and was discharged to home.- - - - - - - - - - ranking = 0.0089584549347328keywords = heart (Clic here for more details about this article) |
7/128. Limb anomalies among offspring of women with a septate uterus: a report of three cases.A retrospective analysis of 467 births among 255 women with uterine malformations revealed that three (0.64%) newborns had limb reduction defects. Two women had a subseptate uterus and one a complete septate uterus with a longitudinal vaginal septum. One newborn had a bilateral split hand and split foot, one had absence of left hand and wrist. One infant born without left hand, wrist and one antebrachial bone associated with omphalocele and diaphragmatic hernia died during the neonatal period. An association between severe limb reduction defects and septate uterus is possible, although the mechanism is unclear. The findings indicate a need to evaluate the uterine cavity if a newborn has this invalid defect, and a detailed ultrasound examination of fetal limbs is warranted in a case of a pregnant septate uterus.- - - - - - - - - - ranking = 0.75keywords = defect (Clic here for more details about this article) |
8/128. pentalogy of cantrell.Omphalocele is often associated with various abnormalities. In two patients admitted with omphalocele, we additionally found defects both in the pars stenalis of diaphragm and in the diaphragmatic surface of the pericardium, sternal defect and tetralogy of fallot. These entities form the components of a syndrome, named pentalogy of cantrell. It is extremely in the spectrum of midline closure defects that display wide variations and its incidence is very low. Existing cardiac defect is the most important factor influencing morbidity and mortality. Herein we report two cases of pentalogy of cantrell with the review of the syndrome in the light of literature.- - - - - - - - - - ranking = 1keywords = defect (Clic here for more details about this article) |
9/128. Revision laparoscopy for incarcerated hernia at a 5-mm trocar site following pediatric laparoscopic surgery.We report the case of a 6-month-old female infant who developed post-operative bowel obstruction due to an incarcerated hernia through a 5-mm laparoscopic wound. The patient underwent laparoscopic Nissen fundoplication for gastroesophageal reflux. On day 6, she showed symptoms of ileus, and the diagnosis of a trocar wound hernia was made on day 13. The herniated intestine was reduced and the defective peritoneum and fascia were closed under relaparoscopic guidance, thus avoiding full-scale laparotomy. A trocar wound hernia causing early postoperative bowel obstruction is a rare complication, especially at 5-mm trocar puncture sites. Intraoperative dislodgment and reinsertion of working trocars may create fascial defects larger than the actual size of the trocar. All laparoscopic puncture wounds, even those <10 mm in size, should be closed at the fascial level in infants. Revision laparoscopy is considered preferable to manage trocar site complications in children.- - - - - - - - - - ranking = 0.5keywords = defect (Clic here for more details about this article) |
10/128. Incisional hernia and fascial defect following laparoscopic surgery.Complications involving the abdominal wall, particularly incisional hernias, were not expected when laparoscopic procedures were first introduced. With the increasing number of laparoscopies in abdominal surgery, more incisional hernias are observed. The authors report 13 cases of umbilical incisional hernia, which occurred late after laparoscopic cholecystectomy, and one case of omental procidentia through a lateral port, which occurred early after laparoscopic hernia repair with the transabdominal preperitoneal technique. There are 4 men and 10 women (mean age, 59.8 years; range, 40-74 years). Between March 1991 and December 1997, a total of 1,287 patients underwent laparoscopic operations at the Surgical Department of the Gradenigo Hospital in Turin, italy. Incisional hernia incidence is 1%. risk factors, such as chronic bronchitis or weight increase, which give rise to endoabdominal pressure, are present in some cases. malnutrition may have a major role in many cases. calculi larger than 15 mm are also seen frequently. Postlaparoscopy incisional hernia is generally a minor complication--only once did its occurrence cause a strangulated hernia. All precautions, including fascial suturing, must be taken to reduce the 1% incidence of postoperative incisional hernias.- - - - - - - - - - ranking = 1keywords = defect (Clic here for more details about this article) |
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