Filter by keywords:



Filtering documents. Please wait...

1/67. torsades de pointes in a case of hypertrophic cardiomyopathy with special reference to the pathologic findings of the heart including the conduction system.

    A clinicopathologic study was performed in a 77-year-old female with hypertrophic cardiomyopathy who had experienced recurrent syncopal attacks due to Torsades de Pointes (TdP) following QT prolongation and atrioventricular block. She died suddenly two years later while eating dinner. Pathologic findings of the heart showed a dilated and hypertrophied left ventricle. The heart weighed 550 g. There were two foci of localized endocardial fibroelastosis (EFE) beneath the aortic valve, one with a size of 3.5 x 3.5 cm, and the other (2 x 1 cm) located on the upper ventricular septum. Histologic findings showed hypertrophy and disarray in the left ventricular myocardium. The conduction system using serial sectioning revealed remarkable bilateral bundle branch fibrosis and hypertrophied purkinje fibers in the left bundle branch adjacent to the EFE on the ventricular septum. These findings were thought to be related to the occurrence of TdP.
- - - - - - - - - -
ranking = 1
keywords = cardiomyopathy
(Clic here for more details about this article)

2/67. Hypertrophic cardiomyopathy: case report.

    A case report of a 19 year old young adult male who died suddenly without any apparent clinical cause is presented. autopsy examination revealed hypertrophied interventricular septum and left ventricle suggestive of a hypertrophic cardiomyopathy (HCM). About 50% of hypertrophic cardiomyopathies are inherited as autosomal dominant disorder, sometimes associated with neuroectodermal syndromes, such as neurofibromatosis and pheochromocytoma. HCM is one of the common causes of severe arrhythmias and sudden death.
- - - - - - - - - -
ranking = 1
keywords = cardiomyopathy
(Clic here for more details about this article)

3/67. Transient right sided hypertrophic cardiomyopathy in an infant born to a diabetic mother.

    Hypertrophic cardiomyopathy (HCM) is a rare primary myocardial disease, characterized by hypertrophy of the left and/or right ventricle. Infants of diabetic mothers (IDM) are at risk for development of HCM, respiratory distress and persistent pulmonary hypertension. A case of severe right sided HCM in an infant born to a diabetic mother is presented. The patient's findings were complementary to the previous observations reporting HCM in IDM. The presence of disproportionate septal hypertrophy in the echocardiography of an infant born to a diabetic mother is highly suggestive of HCM in IDM. In our opinion, further cardiac evaluation is not indicated unless other cardiac abnormalities are suspected.
- - - - - - - - - -
ranking = 1
keywords = cardiomyopathy
(Clic here for more details about this article)

4/67. Apical aneurysm and left ventricular hypertrophy.

    A 59-year-old woman presented with an embolic transient ischemic attack and a history of controlled hypertension for 16 years. Both echocardiogram and MRI showed severe biventricular hypertrophy and an apical aneurysm with a thrombus. The occurrence of an apical aneurysm in the presence of cardiac hypertrophy is a rare finding and has been described in patients with hypertrophic cardiomyopathy. However, it has not been reported in patients with systemic arterial hypertension. In this patient the lack of a relationship between the severity of the hypertrophy and the levels of blood pressure, together with the presence of histologic disorganization of myocardial cardiac muscle cells by endomyocardial biopsy suggested the diagnosis of hypertrophic cardiomyopathy.
- - - - - - - - - -
ranking = 0.4
keywords = cardiomyopathy
(Clic here for more details about this article)

5/67. Anteroapical stunning and left ventricular outflow tract obstruction.

    Dynamic left ventricular outflow tract (LVOT) obstruction is typically observed in the setting of hypertrophic cardiomyopathy. It has also been reported with concentric LV hypertrophy, excessive sympathetic stimulation, and acute myocardial infarction. We describe 3 patients with chest discomfort after emotional stress, who had pronounced abnormalities on electrocardiograms, insignificant obstructive coronary disease and hemodynamic instability with LVOT obstruction, and regional wall motion abnormalities. Suppression of contractility with beta-blockers resulted in resolution of the gradient and in clinical improvement. On follow-up, functional recovery was excellent, and ventricular function had normalized. The conditions and mechanisms that may produce this sequence of events are discussed. The most probable scenario is that an acute ischemic insult secondary to vasospasm, LV stunning, and acute geometric remodeling produced a substrate for LVOT obstruction that was exacerbated by basal LV hypercontractility. The importance of this observation is that routine treatment of cardiogenic shock cannot be used and that conservative management results in excellent prognosis.
- - - - - - - - - -
ranking = 0.2
keywords = cardiomyopathy
(Clic here for more details about this article)

6/67. Anomalous origin of 4 coronary ostia from the right sinus of valsalva in a patient with hypertrophic cardiomyopathy.

    Anomalous origin of 4 separate coronary ostia from a single coronary sinus has rarely been reported. We report what is to our knowledge a previously undescribed variation characterized by the left anterior descending, left ramus, left circumflex, and right coronary arteries originating from separate ostia in the right sinus of valsalva. In addition, the autopsy disclosed features of hypertrophic cardiomyopathy, rarely associated with congenital coronary anomalies.
- - - - - - - - - -
ranking = 1
keywords = cardiomyopathy
(Clic here for more details about this article)

7/67. Two case reports on incessant left ventricular tachycardia: curative therapy with radiofrequency ablation.

    INTRODUCTION: Incessant ventricular tachycardia is a rare arrhythmia which can be life threatening. Treatment with anti-arrhythmic agents may occasionally fail. CLINICAL PICTURE: We report 2 cases of incessant ventricular tachycardia. The first case was a young man with idiopathic left ventricular tachycardia who was in incessant ventricular tachycardia despite treatment with multiple anti-arrhythmic drugs and developed dilated cardiomyopathy. The second case was an asymptomatic girl with the incidental finding of an incessant ventricular tachycardia which originated from the left ventricular outflow tract. TREATMENT AND OUTCOME: Both patients underwent electrophysiologic study and radiofrequency ablation with complete termination of the tachycardia. CONCLUSION: Radiofrequency catheter ablation in experienced centres should be the first-line therapy for incessant ventricular tachycardia.
- - - - - - - - - -
ranking = 0.2
keywords = cardiomyopathy
(Clic here for more details about this article)

8/67. MRI of subendocardial perfusion deficits in isolated left ventricular noncompaction.

    Ventricular noncompaction is a rare unclassified cardiomyopathy due to intrauterine arrest of compaction of the loose interwoven meshwork. It is characterized by markedly irregular endocardial surfaces with prominent trabeculations and intertrabecular recesses. patients are asymptomatic or present with depressed ventricular function, ventricular arrhythmia, and systemic embolism. Areas of restricted myocardial perfusion have been previously documented by scintigraphy and positron emission tomography. This report documents a case of isolated left ventricular noncompaction with subendocardial perfusion deficits on MRI.
- - - - - - - - - -
ranking = 0.2
keywords = cardiomyopathy
(Clic here for more details about this article)

9/67. Regional cardiac sympathetic denervation and systolic compression of a septal perforator branch in a sudden death survivor with hypertrophic cardiomyopathy.

    Hypertrophic cardiomyopathy is a heterogeneous primary cardiac disease with a broad clinical spectrum, including a high risk for sudden death in a certain subgroup of patients. However, the precise criteria for identifying the subgroup at high risk have not been established. The authors describe a 41-year-old man with hypertrophic cardiomyopathy who was examined after an episode of aborted sudden death. Extensive invasive and noninvasive investigations did not reveal a cardiac abnormality other than severe sympathetic denervation in the midbasal septal wall on iodine-123 MIBG SPECT imaging and concentric left ventricular hypertrophy on echocardiography. A retrospective review of the cardiac catheterization findings, however, revealed systolic compression of a septal perforator artery. The aborted sudden death of the patient was most likely associated with systolic compression of a septal branch or sympathetic denervation, which may have precipitated a ventricular arrhythmia in this patient.
- - - - - - - - - -
ranking = 1.2
keywords = cardiomyopathy
(Clic here for more details about this article)

10/67. Noninvasive and invasive evaluation of noncompaction cardiomyopathy.

    Noncompaction cardiomyopathy is a recently described rare congenital cardiomyopathy; patients can be asymptomatic or develop diastolic and/or systolic left ventricular dysfunction with heart failure, systemic emboli or ventricular arrhythmias. Long-term prognosis is poor. Currently, diagnosis is based on findings on 2D echocardiography; in the current case report we demonstrate the use of MRI to diagnose noncompaction cardiomyopathy.
- - - - - - - - - -
ranking = 1.4
keywords = cardiomyopathy
(Clic here for more details about this article)
| Next ->


Leave a message about 'Hypertrophy, Left Ventricular'


We do not evaluate or guarantee the accuracy of any content in this site. Click here for the full disclaimer.