1/16. Congenital unilateral fusion of the maxilla and mandible.We present an uncommon severe first branchial arch congenital malformation, in which complete unilateral bony fusion between the maxillary and mandibular processes was found in a newborn exposed to carbamazepine medication all through pregnancy. This condition interferes with oral feeding, intubation, growth and development. In a review of previously reported cases it was found that this anomaly was commonly associated with other abnormalities. The etiology of this malformation was uncertain in our case, as carbamazepine was not proven to be the definite cause.- - - - - - - - - - ranking = 1keywords = growth (Clic here for more details about this article) |
2/16. A new arthrogryposis syndrome with facial and limb anomalies.A new familial syndrome of facial and limb anomalies was shown in a 4-month-old girl. Small mouth and jaw with limited jaw movement were seen in infancy, with growth to relatively normal size and movement in adulthood, but with a persistent, deep, horizontal depression just above the chin. Mild short stature and microcephaly as well as large ears with lack of the anthelix were present in family members. Severe flexion contractures of the hands and feet were present and led to subluxation of fingers and club feet in the most severely affect child. Marked variability among family members was seen, but a dominant inheritance seems likely.- - - - - - - - - - ranking = 1keywords = growth (Clic here for more details about this article) |
3/16. A novel syndrome with dwarfism, poorly muscled build, absent clavicles, humeroradial fusion, slender bones, oligodactyly and micrognathia.We report on a 15-year-old girl with severe pre- and post-natal growth retardation, poorly muscled build, micrognathia, ulnar ray oligodactyly, absent clavicles, abnormal scapulae, humeroradial fusion, hip dislocation, small iliac wings, slender tubular bones and normal intelligence. An extensive search has failed to ascribe this association to a known condition. This child shared some clinical and radiological features with the Yunis-Varon syndrome but the normal intelligence and the ulnar ray oligodactyly of our patient does not support this diagnosis.- - - - - - - - - - ranking = 1keywords = growth (Clic here for more details about this article) |
4/16. Aesthetic improvements in mid-lower face skeletal surgery.Current surgical techniques allow to correct congenital and acquired facial deformities as well as aesthetic deficiencies resulting from inadequate bone support with excellent functional and aesthetic results. Hard and overlying soft tissue being in a closer anatomic relationship, remarkable aesthetic improvements can be achieved through the three-dimensional shifting of skeletal sections. Hence, facial aesthetic plays such an increasingly critical role in the repair surgery of basal deformities and in the surgical correction of poor aesthetics associated with growth abnormalities as to possibly trespass plastic surgeons' scope of activity. After setting forth our diagnostic and therapeutic guidelines through some relevant clinical cases, the increasingly closer relation between aesthetics enhancement and purely functional surgery of facial muscular and bone structures will be emphasized. Finally, some of the possible treatments currently available will be outlined.- - - - - - - - - - ranking = 1keywords = growth (Clic here for more details about this article) |
5/16. Seventeen-year follow-up of a patient with median cleft of the lower lip, mandible, and tongue with flexion contracture: a case report.PURPOSE: We present a 17-year follow-up of an unusual patient with median cleft of the lower lip, mandible, and tongue with a flexion contracture. CONCLUSION: Timing of the mandibular reconstruction needs to take into account growth of the mandible and masticatory function. In this case, fixation of the mandible performed at the age of 6 years 6 months and reconstruction carried out at 7 years 8 months of age resulted in satisfactory occlusion and masticatory function.- - - - - - - - - - ranking = 1keywords = growth (Clic here for more details about this article) |
6/16. Clinical and radiological evaluation of cherubism: a sporadic case report and review of the literature.Many cases have been published on cherubism since Jones described it first time in three children of the same family [Am. J. Cancer 17 (1933) 946]. cherubism is an autosomal-dominant disorder in which the normal bone is replaced by cellular fibrous tissue and immature bone. Extracranial skeletal involvement is rarely seen in hereditary and non-hereditary forms of the disorder. The mandible is the most severely affected craniofacial component, in which uncontrolled growth of the malady deteriorates the aesthetic balance of the face. Bilateral swelling of the cheeks, mandibular enlargement and maxillary spongious hypertrophy cause orbital manifestations and tendency of eyes looking up to the sky. Thus, the pathognomic clinical feature resembles the appearance of "raised to heaven" Renaissance cherubs. The sporadic case concerns a child affected by cherubism. Radiographic and clinical data of the patient are presented and brief review of the literature is included.- - - - - - - - - - ranking = 1keywords = growth (Clic here for more details about this article) |
7/16. Chincup therapy for a young woman with anterior displacement and obtuse angle of the mandible in Class I malocclusion.INTRODUCTION: Dolichofacial skeletal patterns are a challenge for the orthodontist. Even when treatment for a long-face patient begins before the adolescent growth spurt, excellent compliance is generally needed. The patient whose care is presented here started treatment at age 14. RESULTS: The extraction of 4 premolars, rapid palatal expansion, and excellent compliance wearing a combination occipital and vertical-pull chincup over a 2-year period led to good results at age 16, with minimal dental or skeletal relapse at age 18 years 5 months.- - - - - - - - - - ranking = 1keywords = growth (Clic here for more details about this article) |
8/16. Malignant infantile osteopetrosis: dental effects in paediatric patients. case reports.AIM: Malignant Infantile osteopetrosis is a hereditary pathology caused due to osteoclastic cells which are incapable of carrying out their functions and hence do not resorb osseous tissue where required. Thus the consequence is that during growth phase, the medullary cavities and nervous tissue cavities do not undergo sufficient growth and the corresponding organs do not develop adequately. The aim of this study is to outline the role of the pediatric dentist who has to carry out protocols of primary, secondary, tertiary prevention intervening at many levels. Clinical features and dental effects are described. Two case reports are presented in this study. CONCLUSION: Oral problems of osteopetrosis are delayed tooth eruption, absence of some teeth, malformed teeth, enamel hypoplasia, disturbed dentinogenesis, hypomineralisation of enamel and dentin, propensity for tooth decay, defects of the periodontal membrane, thickened lamina dura, mandibular protrusion, and the presence of odontomas. Tooth removal should be limited as it may induce bone fractures and osteomyelitis. The role of the pediatric dentist is defined.- - - - - - - - - - ranking = 2keywords = growth (Clic here for more details about this article) |
9/16. Congenital fusion of the maxilla and mandible: brief case report.Congenital fusion of the mandible and maxilla is a rare anomaly usually seen in association with various syndromes. Reports of isolated cases of bony fusion of the jaws are sparse. Only 10 reported cases were found in the literature search. Maxillomandibular fusion restricts mouth opening, causing feeding problems and difficulties in swallowing, respiration, growth, and development, and thus must be treated early. We report a case of congenital fusion of the mandible and maxilla in a 1-year-old boy and describe the clinical features of this anomaly to add to the existing literature on the subject. This is our second encounter of such a case.- - - - - - - - - - ranking = 1keywords = growth (Clic here for more details about this article) |
10/16. Bifid mandibular condyle.This report brings the total number of bifid mandibular condyles reported so far in the English-language literature to 15 cases. In addition, one dried specimen with two distinct condylar heads is reported. This rare anomaly does not appear to have a predilection for any particular race or either gender. At the time of initial consultation, almost all patients are adults. Sixty-seven percent of the patients have no complaints related to the affected condyles, but the condition is an incidental dental panoramic radiographic finding. The left condyles seem to be affected twice as often as the right condyles. We do not yet fully know the etiology, epidemiology, and long-term functional effects of this condition. We recommend the transorbital condylar view as a good, inexpensive, and lower dosage technique, compared with the tomogram, to demonstrate this anomaly.- - - - - - - - - - ranking = 0.016779429112592keywords = number (Clic here for more details about this article) |
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