Cases reported "Lymphangiectasis"

Filter by keywords:



Filtering documents. Please wait...

21/53. Familial congenital non-immune hydrops, chylothorax, and pulmonary lymphangiectasia.

    Pulmonary lymphangiectasia is an uncommon congenital anomaly, and familial occurrence has rarely been reported. We report on two sibs with bilateral pleural effusion/chylothorax and hydrops who died neonatally. One sib required prenatal intrauterine hemithoracic drainage. autopsy confirmed congenital pulmonary lymphangiectasia (CPL) histologically in the first case. Hydrops, characterized as subcutaneous edema and effusions in two or more body cavities, may be due to a variety of factors, but the co-occurrence of CPL in one of these sibs, although rare, supports the notion that chylothorax and hydrops may be caused by structural lesions of lymph channels. Although most cases of CPL are sporadic, the reported sibs support autosomal recessive inheritance, with intrafamilial variability of a lymphatic disorder on a genetic basis. Mutations in vascular endothelial growth factor receptor-3 (VEGFR3) in families with Milroy disease, mutations of FOXC2 in the lymphedema-distichiasis syndrome, and fatal chylothorax in alpha9-deficient mice are potential candidate genes.
- - - - - - - - - -
ranking = 1
keywords = lymphatic
(Clic here for more details about this article)

22/53. Endothelial, inducible and neuronal nitric oxide synthase in congenital pulmonary lymphangiectasis.

    Abnormal growth and development of lymphatic pulmonary structures leads to severe hypoxia in congenital pulmonary lymphangiectasis (CPL). This case study aims to determine the cellular source and topographical distribution of the nitric oxide synthases in CPL. It studies the post mortem tissue of a term newborn with the clinical course and histological findings of CPL and three controls without pulmonary pathology. It was found that endothelial cells of pulmonary arteries and lymphatic structures stained significantly more for endothelial nitric oxide synthase protein in the CPL patient compared to the controls. The authors conclude that synthesis of endothelial nitric oxide synthase is upregulated in vascular and lymphatic endothelial cells in congenital pulmonary lymphangiectasis.
- - - - - - - - - -
ranking = 3
keywords = lymphatic
(Clic here for more details about this article)

23/53. Unusual diffuse pulmonary lymphatic proliferation in a young boy.

    We describe a 4-year-old boy who died of an unusual generalized pulmonary lymphatic proliferation. His condition cannot clearly be categorized with any of the previously described pulmonary lymphatic disorders.
- - - - - - - - - -
ranking = 6
keywords = lymphatic
(Clic here for more details about this article)

24/53. Ultrasound findings in retroperitoneal lymphangiomyomatosis.

    A 44-year old female patient with pulmonary lymphangiomyomatosis was examined by standard abdominal sonography. A wide involvement of the retroperitoneal lymph nodes and vessels was found. The relevant sonographic features were enlarged lymph nodes, and multiple anechoic structures, irregular in shape, thin-walled, with intraluminal septa. The findings, which resembled active cysts or liquid-filled bowels, were diagnosed as multiple ectasic lymphatic vessels.
- - - - - - - - - -
ranking = 1
keywords = lymphatic
(Clic here for more details about this article)

25/53. Congenital testicular lymphangiectasis in children with otherwise normal testes.

    Two cases of testicular lymphangiectasis are reported, occurring in stillborns. The disease is a congenital malformation consisting of an abnormal expansive development of lymphatic vessels in both testes. autopsy study revealed the absence of pulmonary, intestinal or systemic lymphangiectasis. The testes showed normal tubular development with normal germ cell numbers and also normal Leydig cell numbers. The epididymis and spermatic cord appeared normal. In contrast with the two previously reported cases of testicular lymphangiectasis, the present cases were not associated with cryptorchidism or other malformations.
- - - - - - - - - -
ranking = 1
keywords = lymphatic
(Clic here for more details about this article)

26/53. Cutaneous lymphangiectases after therapy for carcinoma of the cervix--a case with unusual clinical and histological features.

    Secondary lymphangioma (lymphangiectasis) has been reported as a consequence of lymphatic damage. No specific histological criteria can be used to differentiate primary lymphangioma circumscriptum from lymphangiectasis. We describe a woman who developed lymphangiectases on both non-lymphoedematous upper thighs after hysterectomy and radiation therapy for carcinoma of the cervix. This case differs from the secondary lymphangiomas reported previously in that the vascular channels appeared in newly formed adventitial dermis without histological changes in the epidermis.
- - - - - - - - - -
ranking = 1
keywords = lymphatic
(Clic here for more details about this article)

27/53. Congenital testicular lymphangiectasis.

    Testicular lymphangiectasis are described for the first time in a patient with bilateral inguinal cryptorchidism. A great number of irregular lymphatic channels was observed within the parenchyma and the tunica vasculosa in both testes. Large and numerous anastomosis between the lymphatic vessels of these two areas could also be seen. The MTD and the TFI of the left testis were normal. Both parameters were very low in the right testis. The association of this fact with the greater development of the lymphatic vessels in this testis strongly supports the idea that testicular lymphangiectasis interfere mechanically with the testis tubular development.
- - - - - - - - - -
ranking = 3
keywords = lymphatic
(Clic here for more details about this article)

28/53. Lymph-vessel embolism in a case of Whipple's disease.

    A case of Whipple's disease is described where the lymphatics in the regional lymph nodes appear to be obstructed by embolized macrophages, containing the characteristic PAS positive bacillary material. It is suggested that the regional lymphangiectasia in Whipple's disease may in part result from such cellular embolism.
- - - - - - - - - -
ranking = 1
keywords = lymphatic
(Clic here for more details about this article)

29/53. penicillamine dermatopathy with lymphangiectases. A clinical, immunohistologic, and ultrastructural study.

    The term penicillamine dermatopathy refers to the characteristic hemorrhagic skin lesions found in persons receiving long-term penicillamine therapy for either Wilson's disease or cystinuria. These lesions are thought to develop as a result of faulty collagen and elastin synthesis. We describe a patient with Wilson's disease who developed extensive penicillamine dermatopathy. In addition, histologic, immunochemical, and ultrastructural studies revealed multiple lymphangiectases with blood vessel to lymphatic anastomosis within these lesions, a finding not previously reported. The possible relationship to defective collagen and elastin formation are considered.
- - - - - - - - - -
ranking = 1
keywords = lymphatic
(Clic here for more details about this article)

30/53. Vulval lymphangiectasia.

    Three cases of lymphangiectasia of the vulva are reported. One case followed Wertheim's hysterectomy for carcinoma of the cervix; two other cases had Crohn's disease with perineal involvement. Lymphangiectasia is a secondary phenomenon resulting from obstruction of previously normal lymphatics. This is in contrast with lymphangioma which is an anatomical abnormality. A review of the literature suggests that the vulval skin may be particularly susceptible to the formation of lymphangiectasia, and our patients' experiences suggest that they are easily mis-diagnosed.
- - - - - - - - - -
ranking = 1
keywords = lymphatic
(Clic here for more details about this article)
<- Previous || Next ->


Leave a message about 'Lymphangiectasis'


We do not evaluate or guarantee the accuracy of any content in this site. Click here for the full disclaimer.