11/270. incontinentia pigmenti: overcoming cosmetic challenges.incontinentia pigmenti is a rare syndrome of genetic origin that affects the melanin production of the melanocytes in the epidermis or superficial dermis. It is an X-linked dominate disease with lethality in males. The syndrome presents with skin and dental manifestations similar to ectodermal dysplasia and congenital syphilis. However, dental alternatives for achieving esthetic reconstruction differ. This article illustrates a case of cosmetic rehabilitation of an 18-year-old woman with incontinentia pigmenti.- - - - - - - - - - ranking = 1keywords = dental (Clic here for more details about this article) |
12/270. Macrodontia in association with a contrasting character microdontia.The dental, genetic, radiological and dermatoglyphic findings of a 19-year-old girl showing macrodontia of maxillary permanent central incisors in association with a contrasting character, microdontia of maxillary permanent lateral and mandibular primary central incisors and bilateral absence of maxillary first premolars and missing of the right mandibular second premolar and peg-shaped mandibular primary lateral incisors and canines were presented.- - - - - - - - - - ranking = 0.5keywords = dental (Clic here for more details about this article) |
13/270. Considerations in dental treatment of children with ectodermal dysplasia.Characteristics of ectodermal dysplasia and agammaglobulinemia have been presented and a case in a 6 1/2-year-old boy having both genetic diseases is reported. The child had been mocked by his peers at school. A maxillary overlay denture and mandibular cast denture were constructed using a Baker bar and cast gold thimble crowns. The parents reported that the patients personality changed favorably after dental treatment was completed. He is now 13 years of age, has had his dentures replaced once, and enjous a rather active life with the aid of antibiotics and supplemental globulins.- - - - - - - - - - ranking = 2.5keywords = dental (Clic here for more details about this article) |
14/270. Dental manifestations in severe combined immunodeficiency following bone marrow transplantation.severe combined immunodeficiency (SCID) is a rare primary immunodeficiency disorder with an estimated overall frequency of 1 in 75 000 live births. bone marrow transplantation is the only curative treatment available. Using T cell-depleted HLA non-identical bone marrow requires preconditioning with a short course of cytotoxic chemotherapy. We report severe dental developmental anomalies in three such patients under long-term follow up.- - - - - - - - - - ranking = 0.5keywords = dental (Clic here for more details about this article) |
15/270. Dental findings in three siblings with Morquio's syndrome.Three siblings with Morquo's syndrome are described. Cultured fibroblasts from the youngest sibling demonstrated a total absence of N-acethylgalactosamine-6-sulphate-sulphatase whereas beta-galactocidase activity was normal, thus verifying the diagnosis of MPS-IV A. Dental features such as pointed cusps, spade-shaped incisors, thin enamel and pitted buccal surfaces were observed in all three children. Furthermore, in all three siblings the TMJ was affected with severe resorption of the head of the condyle. Histological examination of exfoliated primary molars showed a band of increased porosity following the striae of Retzius in the outer part of the enamel. These developmental disturbances were occasionally associated with minor localized defects in the enamel surface. The importance of close monitoring of dental development and regular dental care in order to prevent attrition of the teeth, loss of vertical face height and subsequent risk of TMJ dysfunction is emphasized.- - - - - - - - - - ranking = 1keywords = dental (Clic here for more details about this article) |
16/270. incontinentia pigmenti: seven cases with dental manifestations.incontinentia pigmenti (Bloch-Sulzberger syndrome) is an uncommon genodermatosis that usually affects female infants. The condition is characterized by four cutaneous stages and is frequently associated with dental, ocular, central nervous system and structural anomalies. A large case series of seven patients, all female, who presented to the Department of Paediatric dentistry at the Eastman Dental Hospital over the last 16 years is reported. The dental features of these cases were typical and included missing teeth, microdontia and delayed eruption. In two of the seven cases, both maxillary canines were palatally impacted.- - - - - - - - - - ranking = 3keywords = dental (Clic here for more details about this article) |
17/270. A solitary maxillary central incisor treated orthodontically: a case report.The presentation of a solitary maxillary central incisor is reported and its association with other congenital abnormalities discussed. It is an important finding for dental health professionals, since it may indicate the presence of other significant midline congenital abnormalities. It may also indicate the presence of associated disorders that profoundly affect growth and development and which, once identified, may be treated.- - - - - - - - - - ranking = 0.5keywords = dental (Clic here for more details about this article) |
18/270. Talon cusp associated with other dental anomalies--a case report.Talon cusp is an anomalous structure resembling an eagles talon which projects lingually from the cingulum area of an incisor. It is a rare anomaly which is commonly seen in maxillary incisors. This paper is a report of a case of Talon cusp associated with cross-bite and partial anodontia.- - - - - - - - - - ranking = 2keywords = dental (Clic here for more details about this article) |
19/270. Orodental abnormalities in lobster claw syndrome (a type of syndactyly).Lobster Claw syndrome is a type of syndactyly, where abnormalities in the hand-foot region as well as the orodental region occur. A case of a 14-year old boy with this syndrome is presented here.- - - - - - - - - - ranking = 2.5keywords = dental (Clic here for more details about this article) |
20/270. Dental findings in the Schimke immuno-osseous dysplasia.Schimke immuno-osseous dysplasia is a rare autosomal recessive disorder that affects primarily bone, T lymphocytes, kidneys, and skin. The patients have a triangular face, broad nasal bridge, bulbous nose tip, small palpebral fissures, short neck, long upper lip, and low hairline. Dental abnormalities of affected patients have not been discussed in detail. The patient described in this clinical report presented with clinical and radiographic abnormalities that may constitute a diagnostic characteristic in this condition.- - - - - - - - - - ranking = 0.0046535623546433keywords = fissure (Clic here for more details about this article) |
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