FAQ - pseudomyxoma peritonei
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Pseudomyxoma peritonei?

Pseudomyxoma peritonei?
Have you or anyone you know had this or if you are a doctor or nurse could you tell me of your experience ? What do do think are the best treatments /places to go for treatment ? is there a way to cure it or is it always fatal ?

It's a very rare type of cancer usually in the form of a polyp that starts in the appendix. I think it can start in parts of the bowel too. Treatment is usually debulking surgery and IP chemotherapy.  (+ info)

How long can someone live with diognosis pseudomyxoma peritonei?

This is a rare form of cancer.

Here is what I found online...

Pseudomyxoma Peritonei

Here is some information from two UK websites on the sugarbaker procedure and prognosis…

"The (sugarbaker) procedure


Pseudomyxoma peritonei is a rare, borderline malignant, slowly progressing tumour. It arises from the appendix or bowel and spreads throughout the peritoneal cavity, producing a large amount of mucus. Most patients will develop symptoms due to the bulk of the tumour. Most patients will eventually die of this condition, but they often survive for several years.

Standard treatment for this condition is surgical debulking, in which the surgeon attempts to remove as much tumour as possible. Recurrence is common, and therefore repeated debulking operations may be needed.

Patients with pseudomyxoma peritonei may be treated using a ‘watch and wait' policy, using surgery only when unacceptable symptoms or life-threatening complications, such as intestinal obstruction, arise.

Outline of the procedure

The Sugarbaker technique combines complete surgical tumour removal (complete cytoreduction) with intraoperative heated chemotherapy, and is followed by postoperative intraperitoneal chemotherapy The operation takes around 10 hours and includes:

·removal of the right hemicolon, spleen, gallbladder, greater omentum and lesser omentum
·stripping of the peritoneum from the pelvis and diaphragm
·stripping of the tumour from the surface of the liver
·removal of the uterus and ovaries in women
·removal of the rectum in some cases


No controlled studies were found. The studies were of poor quality. One of the studies including 385 patients found 5-year survival to be 86% for those with less malignant pathology (adenomucinosis) and 50% for those with more malignant pathology (mucinous adenocarcinoma). However, not all patients in this study were followed up for 5 years, and it is not clear how survival was calculated. Another study found overall 5-year survival to be around 74% in the 98 out of 321 patients who underwent repeat cytoreductive surgery. For more details, refer to the sources of evidence (see Appendix). "

Re: debulking surgery with concomitant sugarbaker procedure or IPEC (Intraperitoneal perioperative chemotherapy survival rates: “patients median survival is 6 years..with 50 to 70% surviving 5 years and 10-32% for 10 yrs” (see link below for the article)
http://cinahl.com/cexpress/hta/summ/summ807.pdf (about IPEC or sugarbaker procedure and survival rates…have to hit options button and click on minimize popup first and play around with it to read it..set the type size from 40% to about 80% and click on the pages at the left side..kinda tricky to read it..but need adobe reader first)

Here are some links to info and clinical trials for the disease..

Pseudomyxoma Peritonei

http://www.rarediseases.org/search/rdbdetail_abstract.html?disname=Pseudomyxoma%20Peritonei (NORD…scroll down for related support organizations and click on those)
http://www.pmppals.org/ (PMP Pals..for pseumyxoma peritonei and appendiceal cancer)
http://www.pmppals.org/trialsandresearch.htm (clinical trials and research links for Pseudomyoma peritonei and appendiceal cancer)
http://www.cancerhelp.org.uk/help/default.asp?page=5534 (PMP information and overview)
http://www.thedoctorsdoctor.com/diseases/pseudomyxoma_peritonei.htm (a complicated study of PMP patients and prognosis)
http://www.cancer.gov/Templates/db_alpha.aspx?CdrID=44256 (definition of PMP..from NCI)
http://www.clinicaltrials.gov/ct/search;jsessionid=6596A6E31E3541D7E5EB65FCF6FBB0AB?term=Pseudomyxoma+Peritonei&submit=Search (clinical trials for Pseudomyxoma Peritonei )
http://www.wrongdiagnosis.com/p/pseudomyxoma_peritonei/trials.htm#trial (list of current and past clinical trials for pseudomyxoma peritonei)
http://www.clinicaltrials.gov/ct/info/resources (introduction to clinical trials)
http://www.cancer.gov/clinicaltrials/finding/treatment-trial-guide (how to find a cancer treatment trial)

3 books on disease symptoms and treatments

you could also get these books on ebay or amazon or a half price book store. (last two are very similar)..
1.Oxford Handbook of Clinical Medicine
2.Handbook of Diseases (Lippencott)
3.Professional Guide to Diseases (Springhouse)  (+ info)

What is the best place to go for treatment if you have Pseudomyxoma Peritonei?

There is a supportive website for this type of cancer and they provide a list of facilities that have been known to treat this disease. They can answer your questions and point you to the right resources:

PMP Pals' Network
http://www.pmppals.org/  (+ info)

Is there a connection between Agent Orange expose and pseudomyxoma peritonei? Where can I find documentation?

Not that im aware. Soliders whom came in contact with Agent Orange normally are diabetic now and experience joint/muscle pain. (First hand experience here) Though some gave had worse conditions such as cancer, it is possible. pseudomyxoma peritonei is usually connected to coming in contact with asbestos.  (+ info)

Does anyone know of open phase one clinical trials for pseudomyxoma peritonei on the east coast?

We are looking for phase one trials at this point that may help my father beat this or live a longer life. He is in otherwise good health considering. Any information would be greatly appreciated. Surgery is not an option. We tried that route in late December, but were told by the surgeon that the cancer in inoperable at this point because you can not remove the small bowel. He has continued with chemo once a week, and has reacted well to it. In the last round, the large mass actually was reduced by 40%, but the cancer is in the abdominal wall and small & large intestines- appendix was already removed which is where it started.

Any new resources about PMP or this type of cancer would be greatly appreciated!

There is a website with some good information and support for this type of cancer:

The PMP Pals’ Network

PMP Awareness Organization

You might be able to find new info and support from the above groups.

I also have some knowledge of a treatment called cytoreductive surgery and intraperitoneal hyperthermic chemoperfusion that was used for my sons abdominal sarcoma. This treatment is also recommended for Pseudomyxoma Peritoneii, so you might want to investigate further:

University of Pittsburgh Medical Cancer Center

You should ask your fathers oncologist to investigate the above treatment to see if he might be a candidate. He can make a referral or send your fathers scans and records for evaluation.

Good luck. ;-)  (+ info)

what is pseudomyxoma peritonei cancer?

i need to know what type of cancer this is!.was diagnosed with it,doc not sure what type!. please respond/help!!!!

Pseudomyxoma Peritonei is an uncommon tumor known for its' production of mucus in the abdominal cavity. If left untreated, mucin will eventually build up to the point where in compresses vital structures I you need more info,
Here's the website wikipedia.org/wiki/pseudomyxoma peritonei
Unlike most cancers, this disease rarely spreads through the lymphatic system or through the bloodstream. Enven though it is charaterized by mucin and scattered cancer cells in the abdominal cavity but not in the liver or other sites of metastasis. This disease is most associated with cancer of the appendix. There have been efforts made to reclassify this disease or rename it because it is a condition that begins in the appendix. Hope this helps. Guess you will be having your appendix removed. Good luck and God bless.  (+ info)

best hospital in india to treat pseudomyxoma peritonei?

All India Institute of Medical Sciences, New Delhi
For online www.aiims.edu  (+ info)

Pseudomyxoma peritonei?

Have you or anyone you know had this or if you are a doctor or nurse could you tell me of your experience ? What do do think are the best treatments /places to go for treatment ? is there a way to cure it or is it always fatal ?

This is a type of tumor most often associated with cancer of the appendix. There is an excellent support website which provides information about the tumor and some of the best places to go for treatments:


There is a type of surgery called cytoreductive surgery with Hyperthermic intraperitoneal chemotherapy. This essentially an abdominal surgery followed by a heated chemo drug placed directly into the abdominal cavity.

My teenage son had an abdominal sarcoma and underwent the cytoreductive surgery and HIPC successfully. He was in surgery about six hours and ICU for three days, in hospital for a total of 7 days before going home. He had no issues and was cancer free for nine months after the surgery.  (+ info)

What is the best place to go for treatment if you have Pseudomyxoma Peritonei?

Pseudomyxoma Peritonei is an uncommon tumor known for its production of mucus in the abdominal cavity. If left untreated, mucin will eventually build up to the point where it compresses vital structures: the colon, the liver, kidneys, and pancreas.
You may contact PMP Pals Network for advice.  (+ info)

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