An enzyme that catalyzes the oxidative decarboxylation of coproporphyrinogen III to protoporphyrinogen IX by the conversion of two propionate groups to two vinyl groups. It is the sixth enzyme in the 8-enzyme biosynthetic pathway of heme, and is encoded by CPO gene. Mutations of CPO gene result in HEREDITARY COPROPORPHYRIA.


Symptoms and diagnosis

Symptoms:

    


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