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1Complement C2100+ 
2Saccharopine Dehydrogenases77+ 
32-Aminoadipic Acid36+ 
4Aldehyde Dehydrogenase36+ 
5Ketoglutaric Acids26+ 
6Lysine15+ 
7Pyridoxine12+ 
8Succinate-Semialdehyde Dehydrogenase9+ 
9Acyl-CoA Dehydrogenases8+ 
10Acyl-CoA Dehydrogenase7+ 
11Ornithine7+ 
12Aldehyde Oxidoreductases6+ 
13Ketoglutarate Dehydrogenase Complex5+ 
14Glutamate-5-Semialdehyde Dehydrogenase5+ 
15Dihydrolipoamide Dehydrogenase5+ 
16Glutaryl-CoA Dehydrogenase4+ 
173-Hydroxysteroid Dehydrogenases4+ 
18Alcohol Oxidoreductases4+ 
19Betaine4+ 
20Oxidoreductases Acting on CH-CH Group Donors4+ 
21Pipecolic Acids4+ 
22NADH, NADPH Oxidoreductases4+ 
23Carbohydrate Dehydrogenases4+ 
245,10-Methylenetetrahydrofolate Reductase (FADH2)4+ 
25Acyl-CoA Dehydrogenase, Long-Chain3+ 
263-Hydroxyacyl CoA Dehydrogenases3+ 
27Carnitine3+ 
28Oxidoreductases Acting on CH-NH Group Donors3+ 
29Phosphoglycerate Dehydrogenase3+ 
30Butyryl-CoA Dehydrogenase3+ 
31Iron-Sulfur Proteins3+ 
32Riboflavin2+ 
33Cytochrome-B(5) Reductase2+ 
34Electron-Transferring Flavoproteins2+ 
355-Hydroxytryptophan2+ 
36Methylenetetrahydrofolate Reductase (NADPH2)2+ 
37Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase2+ 
38Thiamine2+ 
39Glutarates2+ 
40Oxidoreductases2+ 
41Dihydropteridine Reductase2+ 
42Glutamine1+ 
43Sulfurtransferases1+ 
44L-Lactate Dehydrogenase1+ 
45Molybdoferredoxin1+ 
46Aldehyde Reductase1+ 
47Pyruvate Dehydrogenase Complex1+ 
48Amino Acids1+ 
49Glycine1+ 
50Flavin-Adenine Dinucleotide1+ 
51Fatty Acid Desaturases1+ 
52Dicarboxylic Acids1+ 
53Flavins1+ 
54Serine1+ 
55Methionine1+ 
56NADP1+ 
57Pyruvate Dehydrogenase (Lipoamide)1+ 
58Homocystine1+ 
59Semicarbazides1+ 
60Biopterin1+ 
61Flavin Mononucleotide1+ 
62Glutamates1+ 
63Hydroxybutyrates1+ 
64Biogenic Amines1+ 
65Ketone Oxidoreductases1+ 
66Pyruvate Decarboxylase1+ 
67Levodopa1+ 
68Glucosephosphate Dehydrogenase1+ 
69Malonates1+ 
70Succinate Dehydrogenase1+ 
71Glutathione Reductase1+ 
72Fursultiamin1+ 
73Hydroxymethylglutaryl CoA Reductases1+ 
74Iron1+ 
75Pyruvates1+ 
76Electron Transport Complex II1+ 
77Urea1+ 

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