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Symptoms:
Hyperlysinemias; Alpha-Aminoadipic Semialdehyde Deficiency Disease; Lysine Alpha-Ketoglutarate Reductase Deficiency Disease; Saccharopine Dehydrogenase Deficiency Disease
Fast
Hierarchical
More information
disease
;
hyperlysinemias
;
lysine
Active principles
Rating
Bibliogr.
Expand
1
Complement C2
100
+
2
Saccharopine Dehydrogenases
77
+
3
2-Aminoadipic Acid
36
+
4
Aldehyde Dehydrogenase
36
+
5
Ketoglutaric Acids
26
+
6
Lysine
15
+
7
Pyridoxine
12
+
8
Succinate-Semialdehyde Dehydrogenase
9
+
9
Acyl-CoA Dehydrogenases
8
+
10
Acyl-CoA Dehydrogenase
7
+
11
Ornithine
7
+
12
Aldehyde Oxidoreductases
6
+
13
Ketoglutarate Dehydrogenase Complex
5
+
14
Glutamate-5-Semialdehyde Dehydrogenase
5
+
15
Dihydrolipoamide Dehydrogenase
5
+
16
Glutaryl-CoA Dehydrogenase
4
+
17
3-Hydroxysteroid Dehydrogenases
4
+
18
Alcohol Oxidoreductases
4
+
19
Betaine
4
+
20
Oxidoreductases Acting on CH-CH Group Donors
4
+
21
Pipecolic Acids
4
+
22
NADH, NADPH Oxidoreductases
4
+
23
Carbohydrate Dehydrogenases
4
+
24
5,10-Methylenetetrahydrofolate Reductase (FADH2)
4
+
25
Acyl-CoA Dehydrogenase, Long-Chain
3
+
26
3-Hydroxyacyl CoA Dehydrogenases
3
+
27
Carnitine
3
+
28
Oxidoreductases Acting on CH-NH Group Donors
3
+
29
Phosphoglycerate Dehydrogenase
3
+
30
Butyryl-CoA Dehydrogenase
3
+
31
Iron-Sulfur Proteins
3
+
32
Riboflavin
2
+
33
Cytochrome-B(5) Reductase
2
+
34
Electron-Transferring Flavoproteins
2
+
35
5-Hydroxytryptophan
2
+
36
Methylenetetrahydrofolate Reductase (NADPH2)
2
+
37
Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase
2
+
38
Thiamine
2
+
39
Glutarates
2
+
40
Oxidoreductases
2
+
41
Dihydropteridine Reductase
2
+
42
Glutamine
1
+
43
Sulfurtransferases
1
+
44
L-Lactate Dehydrogenase
1
+
45
Molybdoferredoxin
1
+
46
Aldehyde Reductase
1
+
47
Pyruvate Dehydrogenase Complex
1
+
48
Amino Acids
1
+
49
Glycine
1
+
50
Flavin-Adenine Dinucleotide
1
+
51
Fatty Acid Desaturases
1
+
52
Dicarboxylic Acids
1
+
53
Flavins
1
+
54
Serine
1
+
55
Methionine
1
+
56
NADP
1
+
57
Pyruvate Dehydrogenase (Lipoamide)
1
+
58
Homocystine
1
+
59
Semicarbazides
1
+
60
Biopterin
1
+
61
Flavin Mononucleotide
1
+
62
Glutamates
1
+
63
Hydroxybutyrates
1
+
64
Biogenic Amines
1
+
65
Ketone Oxidoreductases
1
+
66
Pyruvate Decarboxylase
1
+
67
Levodopa
1
+
68
Glucosephosphate Dehydrogenase
1
+
69
Malonates
1
+
70
Succinate Dehydrogenase
1
+
71
Glutathione Reductase
1
+
72
Fursultiamin
1
+
73
Hydroxymethylglutaryl CoA Reductases
1
+
74
Iron
1
+
75
Pyruvates
1
+
76
Electron Transport Complex II
1
+
77
Urea
1
+
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