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11/46. Double-chambered right ventricle associated with mural and pulmonic valve endocarditis: description of a clinical case and review of the literature.

    A double-chambered right ventricle is a relatively uncommon congenital cardiac defect characterized by the presence of anomalous muscle bundles dividing the right ventricle into a high-pressure proximal chamber and a low-pressure distal chamber. This pathology is often wrongly diagnosed in adult patients. We report the first case of a patient with double-chambered right ventricle associated with a mural and pulmonic valve endocarditis caused by streptococcus parasanguis diagnosed with two-dimensional echocardiography. During the course of treatment, the patient suffered from a septic pulmonary embolism, and subsequently required surgical intervention, which confirmed the echocardiographic findings.
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ranking = 1
keywords = cardiac
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12/46. Limited Wegener's granulomatosis presenting with complete heart block.

    Complete heart block associated with Wegener's granulomatosis (WG) is rare, and has not previously been reported with 'limited' WG. The case of a 36-year-old man who presented with complete heart block due to 'limited' WG [positive cytoplasmic antineutrophil cytoplasmic antibodies (c-ANCA) on indirect immunofluorescence, positive serum antibodies to proteinase-3, and inflammatory sinus disease seen on computerized tomography (CT) without renal or pulmonary involvement] is presented. In addition, a gallium-scan fused with a myocardial perfusion scan and cardiac magnetic resonance imaging (MRI) suggested focal inflammation near the atrioventricular (AV) node.
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ranking = 2.672086307196
keywords = cardiac, heart
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13/46. A very rare anatomic variation of the right ventricular branch: right ventricular descending branch from the anterior interventricular branch.

    The anterior interventricular branch of the left coronary artery has the most constant distribution in the human heart and rarely gives off right ventricular branches. Here we report a case with a right ventricular branch which diverged from the anterior interventricular branch and descended on the anterior right ventricular wall parallel to the anterior interventricular sulcus; we termed it the "right ventricular descending branch." This artery gave a collateral artery to the occluded anterior interventricular branch at the apex, and had prevented anterior myocardial infarction. The right ventricular descending branch should be precisely identified in order to perform successful myocardial revascularization procedures such as coronary artery bypass grafting and percutaneous coronary intervention, especially in a patient with anterior interventricular branch occlusion.
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ranking = 0.27868105119933
keywords = heart
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14/46. Tracheal agenesis: management of the first 10 months of life.

    Tracheal agenesis is a potentially lethal congenital anomaly, appearing only at birth. We describe a newborn preterm infant who presented with immediate respiratory distress and no audible cry. There was almost complete tracheal agenesis with a very short segment of distal trachea (only two tracheal rings) arising from the anterior wall of the esophagus, before dividing into the mainstem bronchi. The anomaly was unsuspected prenatally, as the scan showed pyloric atresia and complex congenital cardiac disease. Despite the patient's difficult course, with correction of the rare-associated malformations (cardiac and gastrointestinal tract anomalies), the fact that the child is lively and neurologically normal for her age, requires that we now consider the patency of the airway and the possibility of surgical correction, in accordance with a good quality of life.
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ranking = 2
keywords = cardiac
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15/46. Left ventricular hydatid cyst presenting with acute ischemic stroke: case report.

    Cardiac hydatid cysts are rarely seen. The presentation of an acute stroke secondary to embolization from a cardiac hydatid cyst is also rare. We report a young boy with left ventricular hydatid cyst who presented with acute ischemic stroke.
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ranking = 1
keywords = cardiac
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16/46. Subperiosteal orbital hemorrhage complicating cardiac surgery.

    Subperiosteal orbital hemorrhage (SPOH) following cardiac surgery has not been previously reported. We present a patient who developed diplopia and right eye proptosis immediately after cardiac surgery for a mitral valve repair and coronary artery bypass graft. A computed tomography (CT) study demonstrated a right superior SPOH. The diplopia and proptosis resolved spontaneously within 4 weeks. Follow-up CT showed complete resolution of the SPOH.
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ranking = 21.722550666583
keywords = cardiac surgery, cardiac
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17/46. Biatrial myxoma: rare incidence in cardiac surgery.

    A myxoma is a rare, usually noncancerous primary tumour of the heart. It is the most common benign cardiac tumour in adults, yet has a very low incidence in the cardiac surgery population, representing less than 1% of all cases. Biatrial myxomas are extremely rare, comprising only 2.5% of cardiac myxomas. Myxomas can be fatal due to embolic events or sudden death, however, prognosis after surgery is extremely good. The challenge for health care professionals is early recognition, diagnosis and treatment to prevent life-threatening events. This case presentation describes a gentleman with biatrial myxomas, and further discussion reviews the location, epidemiology, pathology, clinical presentation, assessment, diagnosis, and treatment aspects of cardiac myxomas. Since myxomas are a rare occurrence in cardiac surgery, it is hoped that this report may increase awareness and enhance cardiovascular nurses' understanding and knowledge in caring for the myxoma patient.
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ranking = 25.001231717782
keywords = cardiac surgery, cardiac, heart
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18/46. Spontaneous coronary dissection during postpartum: etiology and controversies in management.

    A 31-year-old female with a history of toxic oil syndrome in childhood, presented with spontaneous left main coronary dissection 4 weeks after an uncomplicated delivery. She had an extensive myocardial infarction, severe left ventricular dysfunction and cardiogenic shock which did not resolve following urgent surgical revascularization. Temporary left ventricular support and heart transplantation were necessary. We analyze the etiology and treatment sequence in what to our knowledge is the first case with these characteristics to be reported.
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ranking = 0.27868105119933
keywords = heart
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19/46. Rate-dependent left bundle branch block during anaesthesia.

    Rate-dependent left bundle branch block during general anaesthesia is rare. Its occurrence makes electrocardiographic diagnosis of acute myocardial ischaemia or infarction difficult. It can also be confused with a slow rate ventricular tachycardia. We present a case of rate-dependent left bundle branch block in a patient with no previous history of ischaemic heart disease. carotid sinus massage resulted in a decrease in heart rate and reversion to normal sinus rhythm.
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ranking = 0.55736210239866
keywords = heart
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20/46. Disseminated microvascular pulmonary tumor cell embolism: a rare cause of fulminant pulmonary hypertension.

    BACKGROUND: Disseminated pulmonary tumor embolization is a rare cause of pulmonary hypertension and is often diagnosed only after the patient has died. CASE REPORT: We report on a 41-year-old male who was admitted because of severe dyspnea and tachycardia. Contrast enhanced spiral computed tomography did neither establish pulmonary thromboembolism nor pulmonary metastasis. Right heart catheterization revealed severe pulmonary hypertension (pulmonary vascular resistance (PVR) 678 dyn x sec x cm(-5)). PVR did not respond to therapy with intravenous nitrate or inhaled iloprost in this critically ill patient. 2 days after admission, the patient died because of refractory right heart failure. autopsy revealed microscopic pulmonary tumor embolism due to a metastasizing adenocarcinoma of the pancreas. CONCLUSION: Disseminated tumor cell embolism should be considered as a rare differential diagnosis in patients with refractory pulmonary hypertension.
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ranking = 0.55736210239866
keywords = heart
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